Management of liver disease and portal hypertension in cystic fibrosis: a review
C Colombo, C Lanfranchi, G Tosetti, F Corti… - Expert Review of …, 2024 - Taylor & Francis
Introduction Cystic fibrosis (CF)-associated liver disease can significantly affect the quality of
life and survival of people with CF. The hepatobiliary manifestations in CF are various, with …
life and survival of people with CF. The hepatobiliary manifestations in CF are various, with …
Evolution of nutritional management in children with cystic fibrosis–a narrative review
C Smith, J Lowdon, J Noordhoek… - Journal of Human …, 2024 - Wiley Online Library
Nutrition has played a central role in the management and outcomes of people with cystic
fibrosis (pwCF) since the 1970s. Advances in therapies and practices in recent decades …
fibrosis (pwCF) since the 1970s. Advances in therapies and practices in recent decades …
Calcium, Phosphorus, and Vitamin D Levels in a Series of Cystic Fibrosis Patients: A Cross-Sectional Study
MF Escobedo-Monge, M Marcos-Temprano… - International Journal of …, 2024 - mdpi.com
Cystic fibrosis (CF) is a monogenic disease with different types of mutations that mainly
affect the respiratory-digestive system. Calcium (Ca), phosphorus (P), and vitamin D (Vit-D) …
affect the respiratory-digestive system. Calcium (Ca), phosphorus (P), and vitamin D (Vit-D) …
Nutritional Trends in Cystic Fibrosis: Insights from the Italian Cystic Fibrosis Patient Registry
Background: Over the past decades, efforts have been made to improve the nutritional well-
being of people with cystic fibrosis (pwCF). Due to the correlation observed between …
being of people with cystic fibrosis (pwCF). Due to the correlation observed between …
Codevelopment of a model of care for adults living with cystic fibrosis‐related diabetes
S Kumar, M Pallin, G Soldatos - Pediatric Pulmonology, 2024 - Wiley Online Library
Background Cystic fibrosis (CF) related diabetes affects up to half of all adults with CF and is
associated with higher morbidity and mortality. Our aim is to codevelop an ideal model of …
associated with higher morbidity and mortality. Our aim is to codevelop an ideal model of …
Improved early growth in Danish children with cystic fibrosis from 2000-2022
K Bader-Larsen, D Faurholt-Jepsen, T Bryrup… - Journal of Cystic …, 2024 - Elsevier
Background Improved growth in children with CF may have resulted from advances in
treatment for cystic fibrosis (CF) over the past two decades, including the implementation of …
treatment for cystic fibrosis (CF) over the past two decades, including the implementation of …
Guiding caregivers of infants with CF in understanding differences in pediatric growth charts
R Bass, C Ren, D Kordunova… - Journal of Cystic …, 2024 - cysticfibrosisjournal.com
International growth charts for children were released by the World Health Organization
(WHO) in 2006, describing weight for age (WFA), length for age (LFA), weight for length …
(WHO) in 2006, describing weight for age (WFA), length for age (LFA), weight for length …
[PDF][PDF] Diabetes asociovaný s cystickou fibrózou–současnost a perspektiva
K Štechová, L Fila - Vnitřní lékařství, 2024 - casopisvnitrnilekarstvi.cz
Cystic fibrosis (CF) is an autosomal recessive inherited disease caused by mutations in the
CFTR gene (the Cystic Fibrosis Transmembrane Conductance Regulator). In most patients …
CFTR gene (the Cystic Fibrosis Transmembrane Conductance Regulator). In most patients …
[PDF][PDF] Sodium Intake of Adults with Cystic Fibrosis Living in North Queensland Post Elexacaftor/Tezacaftor/Ivacaftor
K Herd, A Matson, F Loel, V Moore, I Evans - researchgate.net
BACKGROUND• People with cystic fibrosis (pwCF) risk sodium deficiency, this is increased
for people living in hot and/or humid climates1. The primary factor contributing to sodium …
for people living in hot and/or humid climates1. The primary factor contributing to sodium …