Lymphangioleiomyomatosis: pathogenesis, clinical features, diagnosis, and management
Lymphangioleiomyomatosis (LAM) is a slowly progressive, low-grade, metastasising
neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal …
neoplasm of women, characterised by infiltration of the lung parenchyma with abnormal …
Lymphangioleiomyomatosis—a wolf in sheep's clothing
EP Henske, FX McCormack - The Journal of clinical …, 2012 - Am Soc Clin Investig
Lymphangioleiomyomatosis (LAM) is a rare progressive lung disease of women. LAM is
caused by mutations in the tuberous sclerosis genes, resulting in activation of the mTOR …
caused by mutations in the tuberous sclerosis genes, resulting in activation of the mTOR …
Uterine PEComas: a morphologic, immunohistochemical, and molecular analysis of 32 tumors
JA Bennett, AC Braga, A Pinto… - The American journal …, 2018 - journals.lww.com
Uterine perivascular epithelioid cell tumors (PEComas) are rare neoplasms that may show
overlapping morphology and immunohistochemistry with uterine smooth muscle tumors. In …
overlapping morphology and immunohistochemistry with uterine smooth muscle tumors. In …
Diffuse cystic lung disease. Part I
N Gupta, R Vassallo… - American journal of …, 2015 - atsjournals.org
The diffuse cystic lung diseases (DCLDs) are a group of pathophysiologically heterogenous
processes that are characterized by the presence of multiple spherical or irregularly shaped …
processes that are characterized by the presence of multiple spherical or irregularly shaped …
Single-cell transcriptomic analysis identifies a unique pulmonary lymphangioleiomyomatosis cell
Rationale: Lymphangioleiomyomatosis (LAM) is a metastatic neoplasm of reproductive-age
women associated with mutations in tuberous sclerosis complex genes. LAM causes cystic …
women associated with mutations in tuberous sclerosis complex genes. LAM causes cystic …
Lymphangioleiomyomatosis: calling it what it is: a low-grade, destructive, metastasizing neoplasm
Lymphangioleiomyomatosis (LAM) is a progressive cystic lung disease primarily affecting
women that has historically been classified and clinically managed as a nonneoplastic …
women that has historically been classified and clinically managed as a nonneoplastic …
Lymphangioleiomyomatosis screening in women with tuberous sclerosis
CJ Cudzilo, RD Szczesniak, AS Brody, MS Rattan… - Chest, 2013 - Elsevier
Background Lymphangioleiomyomatosis (LAM) occurs in at least 40% of women with
tuberous sclerosis complex (TSC), as diagnosed based on chest CT scan findings. Early …
tuberous sclerosis complex (TSC), as diagnosed based on chest CT scan findings. Early …
Lymphangioleiomyomatosis
SR Johnson - Orphan lung diseases: a clinical guide to rare lung …, 2023 - Springer
Lymphangioleiomyomatosis (LAM) is a rare multisystem disease which predominantly
affects women. The disease occurs both sporadically and is common in women with …
affects women. The disease occurs both sporadically and is common in women with …
Clinical features, epidemiology, and therapy of lymphangioleiomyomatosis
AM Taveira-DaSilva, J Moss - Clinical epidemiology, 2015 - Taylor & Francis
Lymphangioleiomyomatosis (LAM) is a multisystem disease of women, characterized by
proliferation of abnormal smooth muscle-like LAM cells, leading to the formation of lung …
proliferation of abnormal smooth muscle-like LAM cells, leading to the formation of lung …
Perivascular epithelioid cell tumors (PEComa) of the gynecologic tract
JA Bennett, E Oliva - Genes, Chromosomes and Cancer, 2021 - Wiley Online Library
PEComas of the female genital tract are rare mesenchymal neoplasms that are most
common in the uterus, but also may occur in other gynecologic locations. As they …
common in the uterus, but also may occur in other gynecologic locations. As they …