Systemic amyloidosis is a rare protein misfolding and deposition disorder leading to
progressive organ failure. There are over 15 types of systemic amyloidosis, each caused by …

Advances in cardiac imaging have resulted in greater recognition of cardiac amyloidosis in
everyday clinical practice, but the diagnosis continues to be made in patients with late-stage …

Objectives This study aimed to investigate the accuracy of a broad range of
echocardiographic variables to develop multiparametric scores to diagnose CA in patients …

Objective To describe the clinical and laboratory characteristics of patients with meticulously
typed light chain (AL) amyloidosis. Patients and Methods Patients (N= 592) with biopsy …

Amyloid light chain (AL) amyloidosis is a rare, debilitating, often fatal disease. Symptoms of
cardiomyopathy are common presenting features, and patients often are referred to …

Transthyretin amyloid cardiomyopathy (ATTR-CM) is a progressively debilitating, rare
disease associated with high mortality. ATTR-CM occurs when TTR amyloid protein builds …

Improvement in survival in Light chain (AL) amyloidosis has been seen over recent decades,
enabling more patients to achieve long‐term survival. Patients with AL amyloidosis who …

Introduction: The diagnosis of amyloidosis requires histological confirmation of Congo-red
(CR) deposits. The tissue source is preferably fat aspiration and/or bone marrow (BM) …

Abstract Purpose of Review Transthyretin (TTR)-related cardiac amyloidosis is a progressive
infiltrative cardiomyopathy that mimics hypertensive, hypertrophic heart disease and may go …

Background and purpose Amyloid myopathy frequently occurs in the setting of systemic
amyloidosis and less commonly in isolation (isolated amyloid myopathy). Anoctaminopathy …