The great advances in the knowledge of inherited thrombocytopenias (ITs) made since the
turn of the century have significantly changed our view of these conditions. To date, ITs …

The new techniques of genetic analysis have made it possible to identify many new forms of
inherited thrombocytopenias (IT) and study large series of patients. In recent years, this has …

Rare bleeding disorders (RBDs) are a heterogeneous group of coagulation factor
deficiencies that include fibrinogen, prothrombin, α 2-antiplasmin, plasminogen activator …

Introduction Women with inherited platelet receptor defects (IPRD) may have an increased
risk of heavy menstrual bleeding (HMB) and postpartum haemorrhage (PPH). Aim To …

Bernard-Soulier Syndrome - StatPearls - NCBI Bookshelf US flag An official website of the
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Bernard–Soulier syndrome (BSS) is a rare congenital bleeding disorder characterized by
thrombocytopenia and giant platelets that display impaired or absent platelet agglutination …

Recombinant factor VIIa (rFVIIa) is a pro-haemostatic agent that is effective in the treatment
of bleeding in haemophilia complicated by inhibitors and some other haemorrhagic …

Abstract Women with Bernard-Soulier syndrome (BSS) are considered to be at high risk of
serious bleeding during childbirth. Due to the frequently occurring platelet transfusion …

The etiologies of thrombocytopenia in patients presenting for cardiac surgery are extensive,
but clinically relevant conditions generally can be categorized by those related to decreased …

Bernard-Soulier syndrome (BSS) is an autosomal recessive inherited bleeding disorder
characterized by prolonged bleeding time, thrombocytopenia, and giant platelets. Patients …