Evaluation and management of the child and adult with Fontan circulation: a scientific statement from the American Heart Association

J Rychik, AM Atz, DS Celermajer, BJ Deal… - Circulation, 2019 - Am Heart Assoc
It has been 50 years since Francis Fontan pioneered the operation that today bears his
name. Initially designed for patients with tricuspid atresia, this procedure is now offered for a …

Fontan-associated liver disease: screening, management, and transplant considerations

J Emamaullee, AN Zaidi, T Schiano, J Kahn… - Circulation, 2020 - Am Heart Assoc
Surgical innovation and multidisciplinary management have allowed children born with
univentricular physiology congenital heart disease to survive into adulthood. An estimated …

Canadian Cardiovascular Society 2022 guidelines for cardiovascular interventions in adults with congenital heart disease

A Marelli, L Beauchesne, J Colman, R Ducas… - Canadian Journal of …, 2022 - Elsevier
Interventions in adults with congenital heart disease (ACHD) focus on surgical and
percutaneous interventions in light of rapidly evolving ACHD clinical practice. To bring rigour …

Hypoplastic left heart syndrome: from fetus to fontan

PP Roeleveld, DM Axelrod, D Klugman… - Cardiology in the …, 2018 - cambridge.org
The care of children with hypoplastic left heart syndrome is constantly evolving. Prenatal
diagnosis of hypoplastic left heart syndrome will aid in counselling of parents, and selected …

Fontan patient survival after pediatric heart transplantation has improved in the current era

KE Simpson, E Pruitt, JK Kirklin, DC Naftel… - The Annals of thoracic …, 2017 - Elsevier
Background Historically, patients with a prior Fontan procedure for complex congenital heart
disease (CHD) have been considered at higher risk for death after heart transplant (HT) …

Advanced Heart Failure Therapies for Adults With Congenital Heart Disease: JACC State-of-the-Art Review

MM Givertz, EM DeFilippis, MJ Landzberg… - Journal of the American …, 2019 - jacc.org
In the contemporary era, nearly 85% of children with congenital heart disease will reach
adulthood. Despite optimal medical and surgical treatment, many will experience a …

[HTML][HTML] Fontan-associated liver disease: Diagnosis, surveillance, and management

C de Lange, T Möller, H Hebelka - Frontiers in pediatrics, 2023 - frontiersin.org
The Fontan operation is a lifesaving procedure for patients with functional single-ventricle
congenital heart disease, where hypoplastic left heart syndrome is the most frequent …

EASL-ERN position paper on liver involvement in patients with Fontan-type circulation

L Téllez, A Payancé, E Tjwa, MJ Del Cerro, L Idorn… - Journal of …, 2023 - Elsevier
Fontan-type surgery is the final step in the sequential palliative surgical treatment of infants
born with a univentricular heart. The resulting long-term haemodynamic changes promote …

Heart transplant indications, considerations, and outcomes in Fontan patients: age-related nuances, transplant listing, and disease-specific indications

AI Dipchand, O Honjo, R Alonso-Gonzalez… - Canadian Journal of …, 2022 - Elsevier
Abstract In the current era, 5%-10% of Fontan patients die or need a transplant in childhood,
and approximately 50% will experience the same fate by age 40 years. Heart transplant …

[HTML][HTML] Transplantation of the failing Fontan

AD McCormick, KR Schumacher - Translational Pediatrics, 2019 - ncbi.nlm.nih.gov
Half a century has passed since the original Fontan palliation. In the interim, surgical and
medical advancements have allowed more single ventricle patients to reach Fontan and …