Background The goal of managing auditory neuropathy spectrum disorder (ANSD) is to
restore the children's ability to discriminate auditory information. Children who are not …

Introduction Sensorineural hearing impairment (SNHI), a common childhood disorder with
heterogeneous genetic causes, can lead to delayed language development and …

Auditory neuropathy spectrum disorder (ANSD) is a hearing impairment involving
disruptions to inner hair cells (IHCs), ribbon synapses, spiral ganglion neurons (SGNs) …

Background: Auditory neuropathy (AN) is a nosological entity of unknown etiology, which is
associated with fluctuations in rates of speech discrimination. Its diagnosis is based on …

Objective: This study assessed the relationship between electrophysiological measures of
the electrically evoked compound action potential (eCAP) and speech perception scores …

Cochlear implantation is the treatment of choice for children with profound sensorineural
hearing impairment (SNHI), yet the outcomes of cochlear implants (CI) vary significantly …

Objective Cochlear nerve deficiency (CND) accounts for about one-third of congenital
hearing loss cases and presents several challenges during management. Currently …

Auditory neuropathy (AN) is a unique type of language developmental disorder, with no
precise rate of genetic contribution that has been deciphered in a large cohort. In a …

Background Wolfram syndrome type 1 gene (WFS1), which encodes a transmembrane
structural protein (wolframin), is essential for several biological processes, including proper …

Cochlear implantation (CI) for deafblindness may have more impact than for non-syndromic
hearing loss. Deafblind patients have a double handicap in a society that is more and more …