During the past quarter century, the diagnosis and treatment of cystic fibrosis (CF) have
been transformed by molecular sciences that initiated a new era with discovery of the cystic …

This is the final of four papers updating standards for the care of people with CF. That this
paper “Planning a longer life” was considered necessary, highlights how much CF care has …

People with cystic fibrosis (CF) are at risk for dysglycaemia caused by progressive beta cell
dysfunction and destruction due to pancreatic exocrine disease and fibrosis. CF-related …

Interdisciplinary teams care for people with cystic fibrosis (pwCF) at specialized treatment
centers. These teams have laid the foundation for the cystic fibrosis (CF) care model …

Cystic fibrosis (CF) is a genetic disease caused by variants in the gene encoding for the CF
transmembrane conductance regulator (CFTR) protein, a chloride and bicarbonate channel …

Objective The objective of this study was to describe reported adverse events (AEs)
associated with elexacaftor/tezacaftor/ivacaftor (ETI) in a pediatric sample with cystic fibrosis …

Bacterial infections of the lower airways are the main cause of mortality and morbidity in
cystic fibrosis. The most frequently isolated pathogens are S. aureus and P. aeruginosa; …

Interest in the transition of care for cystic fibrosis (CF) patients has grown significantly over
time, driven by advancements in treatment that have extended life expectancy. As more CF …

The major cause of mortality in people with cystic fibrosis (pwCF) is progressive lung
disease characterised by acute and chronic infections, the accumulation of mucus, airway …

“My health care team and I can be very honest with each other. I always feel like they really
care about me and the outcome of whatever problem is at hand. It is hard trusting someone …