The lung in inborn errors of immunity: From clinical disease patterns to molecular pathogenesis

MJ Gutierrez, G Nino, D Sun… - Journal of Allergy and …, 2022 - Elsevier
In addition to being a vital organ for gas exchange, the lung is a crucial immune organ
continuously exposed to the external environment. Genetic defects that impair immune …

Partial Anomalous Left Pulmonary Artery Anterior Versus Posterior Types: A Systematic Review

CS Restrepo, TV Gonzalez, AJ Baxi, SS Saboo - Tomography, 2022 - mdpi.com
The aim of this study was to investigate the features of partial anomalous left pulmonary
artery (PALPA) and differences between cases with posterior versus anterior a nomalous …

An unusual presentation of Kabuki syndrome with orbital cysts, microphthalmia, and cholestasis with bile duct paucity

N Bögershausen, U Altunoglu… - American Journal of …, 2016 - Wiley Online Library
Kabuki syndrome (KS) is a rare developmental disorder characterized by multiple congenital
malformations, postnatal growth retardation, intellectual disability, and recognizable facial …

Postoperative nursing care of a child with pulmonary artery displacement combined with slide tracheobronchial plasty

C Jin, N Lin, S Yang, C Yan, S Li, X Wu… - Nursing in Critical …, 2023 - Wiley Online Library
Generally, pulmonary artery sling operation involves the pulmonary artery transplantation to
be cut off. Nursing care is focused on the postoperative pulmonary vascular anastomosis …

[HTML][HTML] Partial anomalous left pulmonary artery sling in an adult

PD Maldjian, KR Adams - Journal of Clinical Imaging Science, 2020 - ncbi.nlm.nih.gov
We report a case of a partial anomalous left pulmonary artery sling in an adult patient as an
incidental finding on computed tomography. There is a normal bifurcation of the pulmonary …

Multislice computed tomography assessment of tracheobronchial patterns in partial anomalous left pulmonary artery

SY Wang, W Gao, YM Zhong, AM Sun… - Journal of Computer …, 2017 - journals.lww.com
Objective The aim of this study was to present relationship between partial anomalous left
pulmonary artery (PALPA) and the tracheobronchial tree and patterns of the …

[HTML][HTML] Arterial tortuosity syndrome: An extremely rare disease presenting as a mimic of pulmonary sling

A Farkas, M Steiner, H Giles, K Miller - Radiology Case Reports, 2018 - Elsevier
Pulmonary sling is the anatomic variant defined by the aberrant origin of the left pulmonary
artery from the right pulmonary artery. This patient presented with a mimic of pulmonary sling …

A left pulmonary artery sling with left bronchiectasis in an adult patient: A case report and review of literature

L Lv, X Cheng, X Yu, C Cui, W Ji… - Respirology Case …, 2023 - Wiley Online Library
Pulmonary artery sling (PAS) is a rare congenital vascular anomaly, and is usually
diagnosed during the infantile or fetal period. Adult presentation of PAS is rare. We report a …

Clinical and imaging features of pulmonary artery sling: The experience in one major medical center

M Yao, Y Li, SI Ali, M Xie, Q Lv - Echocardiography, 2018 - Wiley Online Library
This case series describes echocardiographic and computed tomography angiographic
(CTA) characteristics, clinical features, diagnosis, and treatment in 15 patients of Pulmonary …

Partial anomalous left pulmonary artery in heterotaxy syndrome. A case report and review of literature

LG Betancourt, HR Singh, A Agarwal - Progress in Pediatric Cardiology, 2021 - Elsevier
Partial anomalous left pulmonary artery in association with congenital heart defects is a rare
anomaly that can cause compression of the tracheobronchial tree. We report a case of …