Diagnostic criteria for Susac syndrome

I Kleffner, J Dörr, M Ringelstein, CC Gross… - Journal of Neurology …, 2016 - jnnp.bmj.com
Background Susac syndrome is characterised by the triad of encephalopathy with or without
focal neurological signs, branch retinal artery occlusions and hearing loss. Establishment of …

Management of stroke in infants and children: a scientific statement from a Special Writing Group of the American Heart Association Stroke Council and the Council on …

ES Roach, MR Golomb, R Adams, J Biller, S Daniels… - Stroke, 2008 - Am Heart Assoc
Purpose—The purpose of this statement is to review the literature on childhood stroke and to
provide recommendations for optimal diagnosis and treatment. This statement is intended …

Susac syndrome: challenges in the diagnosis and treatment

M Marrodan, MP Fiol, J Correale - Brain, 2022 - academic.oup.com
Susac syndrome is a disorder thought to be mediated by an autoimmune response towards
endothelial cells, leading to a characteristic clinical triad of encephalopathy, visual …

White matter diseases with radiologic-pathologic correlation

N Sarbu, RY Shih, RV Jones, I Horkayne-Szakaly… - Radiographics, 2016 - pubs.rsna.org
White matter diseases include a wide spectrum of disorders that have in common
impairment of normal myelination, either by secondary destruction of previously myelinated …

Characteristics of Susac syndrome: a review of all reported cases

J Dörr, S Krautwald, B Wildemann, S Jarius… - Nature Reviews …, 2013 - nature.com
In Susac syndrome, occlusions of microvessels—presumed to be mediated by an
autoimmune response to an as yet unknown antigen—lead to a characteristic clinical triad of …

MRI and the diagnosis of multiple sclerosis: expanding the concept of “no better explanation”

A Charil, TA Yousry, M Rovaris, F Barkhof… - The Lancet …, 2006 - thelancet.com
Although the diagnosis of multiple sclerosis relies on the demonstration of disease
dissemination in space and time, the exclusion of other neurological disorders is also …

[HTML][HTML] Leptomeningeal enhancement in multiple sclerosis and other neurological diseases: A systematic review and Meta-Analysis

BV Ineichen, C Tsagkas, M Absinta, DS Reich - NeuroImage: Clinical, 2022 - Elsevier
Background The lack of systematic evidence on leptomeningeal enhancement (LME) on
MRI in neurological diseases, including multiple sclerosis (MS), hampers its interpretation in …

Susac's syndrome—update

R Rennebohm, JO Susac, RA Egan… - Journal of the neurological …, 2010 - Elsevier
Susac's Syndrome (SS) consists of the clinical triad of encephalopathy, branch retinal artery
occlusion (BRAO), and hearing loss (HL). It is an autoimmune endotheliopathy affecting the …

Susac's syndrome: 1975–2005 microangiopathy/autoimmune endotheliopathy

JO Susac, RA Egan, RM Rennebohm… - Journal of the neurological …, 2007 - Elsevier
Susac's syndrome (SS) consists of the clinical triad of encephalopathy, branch retinal artery
occlusions (BRAO) and hearing loss. It is due to a microangiopathy affecting the precapillary …

Lesion morphology at 7 Tesla MRI differentiates Susac syndrome from multiple sclerosis

J Wuerfel, T Sinnecker, EB Ringelstein… - Multiple Sclerosis …, 2012 - journals.sagepub.com
Background: Although an orphan disease with still obscure aetiopathogenesis, Susac
syndrome has to be considered as differential diagnosis in multiple sclerosis (MS), since its …