Purpose Neuroendocrine neoplasms can occur as part of inherited disorders, usually in the
form of well-differentiated, slow-growing tumors (NET). The main predisposing syndromes …

Renal cell carcinoma is a heterogenous cancer composed of an increasing number of
unique subtypes each with their own cellular and tumor behavior. The study of hereditary …

Objective The aim of this review is to provide a practical approach for clinicians regarding
the diagnosis and management of pheochromocytomas and paragangliomas (PPGL) …

Simple Summary Neuroendocrine neoplasms (NENs) are tumors originating from
neuroendocrine cells, with increasing global incidence and prevalence. Radioligand …

Simple Summary Von Hippel–Lindau (VHL) is a hereditary syndrome associated with
various tumors in the brain, spine, eyes, kidneys, adrenals, and in the pancreas …

Von Hippel-Lindau (VHL) disease is an autosomal dominant condition that predisposes
affected individuals to a variety of malignant and benign neoplasms. The pathogenetic …

Adrenocortical carcinoma (ACC) and pheochromocytoma/paraganglioma (PPGL) are two
rare types of adrenal gland malignancies. Regarding hereditary tumors, some patients with …

Simple Summary Von Hippel–Lindau is a rare endocrine (and other organ) multi-neoplasia
syndrome. A clinical diagnosis may be defined using different diagnostic criteria. However …

Abstract Von Hippel–Lindau disease (VHL) is a multisystem cancer syndrome caused by the
inactivation of the VHL tumor suppressor gene and involves various organ systems …

Simple Summary Renal cancer is a common malignant neoplasm. Indeed, not every cancer
is created equal, as there are different entities with specific morphological and molecular …