The toxicity of nanoparticles and their interaction with cells: an in vitro metabolomic perspective

M Awashra, P Młynarz - Nanoscale Advances, 2023 - pubs.rsc.org
Nowadays, nanomaterials (NMs) are widely present in daily life due to their significant
benefits, as demonstrated by their application in many fields such as biomedicine …

Omics approaches for the assessment of biological responses to nanoparticles

Y Abdelkader, L Perez-Davalos, R LeDuc… - Advanced Drug Delivery …, 2023 - Elsevier
Nanotechnology has enabled the development of innovative therapeutics, diagnostics, and
drug delivery systems. Nanoparticles (NPs) can influence gene expression, protein …

Oxidation of alpha-ketoglutarate is required for reductive carboxylation in cancer cells with mitochondrial defects

AR Mullen, Z Hu, X Shi, L Jiang, LK Boroughs… - Cell reports, 2014 - cell.com
Mammalian cells generate citrate by decarboxylating pyruvate in the mitochondria to supply
the tricarboxylic acid (TCA) cycle. In contrast, hypoxia and other impairments of …

Hypoxia-mediated increases in L-2-hydroxyglutarate coordinate the metabolic response to reductive stress

WM Oldham, CB Clish, Y Yang, J Loscalzo - Cell metabolism, 2015 - cell.com
Metabolic adaptation to hypoxia is critical for survival in metazoan species for which reason
they have developed cellular mechanisms for mitigating its adverse consequences. Here …

Clinical metabolomics: the new metabolic window for inborn errors of metabolism investigations in the post-genomic era

A Tebani, L Abily-Donval, C Afonso, S Marret… - International journal of …, 2016 - mdpi.com
Inborn errors of metabolism (IEM) represent a group of about 500 rare genetic diseases with
an overall estimated incidence of 1/2500. The diversity of metabolic pathways involved …

Genetic basis of mitochondrial diseases

M Gusic, H Prokisch - FEBS letters, 2021 - Wiley Online Library
Mitochondrial disorders are monogenic disorders characterized by a defect in oxidative
phosphorylation and caused by pathogenic variants in one of over 340 different genes. The …

Metabolomics of mitochondrial disease

K Esterhuizen, FH Van der Westhuizen, R Louw - Mitochondrion, 2017 - Elsevier
Mitochondrial disease (MD) diagnostics and disease progression investigations have
traditionally relied very little on metabolic data, due to a lack of biomarker sensitivity and …

Quantitative metabolic flux analysis reveals an unconventional pathway of fatty acid synthesis in cancer cells deficient for the mitochondrial citrate transport protein

L Jiang, A Boufersaoui, C Yang, B Ko, D Rakheja… - Metabolic …, 2017 - Elsevier
The mitochondrial citrate transport protein (CTP), encoded by SLC25A1, accommodates
bidirectional trafficking of citrate between the mitochondria and cytosol, supporting lipid …

DNA methylation associated with mitochondrial dysfunction in a South African autism spectrum disorder cohort

S Stathopoulos, R Gaujoux, Z Lindeque… - Autism …, 2020 - Wiley Online Library
Autism spectrum disorder (ASD) is characterized by phenotypic heterogeneity and a
complex genetic architecture which includes distinctive epigenetic patterns. We report …

[HTML][HTML] Mitochondrial stress causes neuronal dysfunction via an ATF4-dependent increase in L-2-hydroxyglutarate

RJ Hunt, L Granat, GS McElroy, R Ranganathan… - Journal of Cell …, 2019 - rupress.org
Mitochondrial stress contributes to a range of neurological diseases. Mitonuclear signaling
pathways triggered by mitochondrial stress remodel cellular physiology and metabolism …