Considerations for advanced heart failure consultation in individuals with Fontan circulation: recommendations from ACTION

AM Lubert, A Cedars, CS Almond, S Amdani… - Circulation: Heart …, 2023 - Am Heart Assoc
Individuals with Fontan circulation are at risk of late mortality from both cardiac and
noncardiac causes. Despite the known risk of mortality, referral indications for advanced …

Fontan-associated liver disease: Diagnosis, surveillance, and management

C de Lange, T Möller, H Hebelka - Frontiers in pediatrics, 2023 - frontiersin.org
The Fontan operation is a lifesaving procedure for patients with functional single-ventricle
congenital heart disease, where hypoplastic left heart syndrome is the most frequent …

Exercise capacity, NT-proBNP, and exercise hemodynamics in adults post-Fontan

WR Miranda, CC Jain, BA Borlaug, AS Jaffe… - Journal of the American …, 2023 - jacc.org
Background Cardiopulmonary exercise testing (CPET) and N-terminal pro–B-type natriuretic
peptide (NT-proBNP) measurement are frequently performed in adults post-Fontan, but their …

Exercise‐induced changes in pulmonary artery wedge pressure in adults post‐Fontan versus heart failure with preserved ejection fraction and non‐cardiac dyspnoea

WR Miranda, BA Borlaug, CC Jain… - European journal of …, 2023 - Wiley Online Library
Aims Despite their universal predisposition, diagnosing diastolic dysfunction in patients post‐
Fontan palliation is challenging. Our aim was to compare exercise haemodynamics between …

The “Super-Fontan” phenotype: characterizing factors associated with high physical performance

DL Tran, DS Celermajer, J Ayer, L Grigg… - Frontiers in …, 2021 - frontiersin.org
Background: People with a Fontan circulation usually have moderately impaired exercise
performance, although a subset have high physical performance (“Super-Fontan”), which …

EASL-ERN position paper on liver involvement in patients with Fontan-type circulation

L Téllez, A Payancé, E Tjwa, MJ Del Cerro, L Idorn… - Journal of …, 2023 - Elsevier
Fontan-type surgery is the final step in the sequential palliative surgical treatment of infants
born with a univentricular heart. The resulting long-term haemodynamic changes promote …

Health‐Related Quality of Life and Its Association With Outcomes in Adults With Congenital Heart Disease and Heart Failure: Insight From FRESH‐ACHD Registry

R Ly, C Karsenty, P Amedro, S Cohen… - Journal of the …, 2023 - Am Heart Assoc
Background Quality of Life (QoL) is a prognostic factor in heart failure (HF) of patients with
acquired cardiac disease. The aim of this study was to determine the predictive value of QoL …

Heart transplant indications, considerations, and outcomes in Fontan patients: age-related nuances, transplant listing, and disease-specific indications

AI Dipchand, O Honjo, R Alonso-Gonzalez… - Canadian Journal of …, 2022 - Elsevier
Abstract In the current era, 5%-10% of Fontan patients die or need a transplant in childhood,
and approximately 50% will experience the same fate by age 40 years. Heart transplant …

Haemodynamic performance of 16–20-mm extracardiac Goretex conduits in adolescent Fontan patients at rest and during simulated exercise

FM Rijnberg, LC van 't Hul… - European Journal of …, 2023 - academic.oup.com
OBJECTIVES To date, it is not known if 16–20-mm extracardiac conduits are outgrown
during somatic growth from childhood to adolescence. This study aims to determine total …

Late Fontan circulatory failure. What drives systemic venous congestion and low cardiac output in adult Fontan patients?

A Van De Bruaene, G Claessen, T Salaets… - Frontiers in …, 2022 - frontiersin.org
The Fontan circulation provides definite palliation for children born with a single anatomical
or functional ventricle by diverting systemic venous blood directly to the pulmonary arteries …