Primary melanocytic tumors of the central nervous system: a review with focus on molecular aspects

HVN Küsters‐Vandevelde, B Küsters… - Brain …, 2015 - Wiley Online Library
Primary melanocytic tumors of the central nervous system (CNS) represent a spectrum of
rare tumors. They can be benign or malignant and occur in adults as well as in children, the …

Neurocutaneous melanocytosis (melanosis)

M Ruggieri, A Polizzi, S Catanzaro, ML Bianco… - Child's Nervous …, 2020 - Springer
Abstract Neurocutaneous melanosis (NCM; MIM# 249400; ORPHA: 2481], first reported by
the Bohemian pathologist Rokitansky in 1861, and now more precisely defined as …

Therapeutic Strategies in Neurocutaneous Melanocytosis

D Basu - Anticancer Research, 2024 - ar.iiarjournals.org
Neurocutaneous melanocytosis (NCM) is a rare, congenital condition primarily affecting
children, characterized by large or giant congenital melanocytic nevi (L/GCMN) on the skin …

The dual PI3K/mToR inhibitor omipalisib/GSK2126458 inhibits clonogenic growth in oncogenically-transformed cells from neurocutaneous melanocytosis

D Basu, CM Salgado, B Bauer, Y Khakoo… - Cancer Genomics & …, 2018 - cgp.iiarjournals.org
Background: Omipalisib has been found to affect the viability of cancer cells. However, its
effect on clonogenicity–a feature of cancer stem cells, is not clear. Cells isolated from …

NRASQ61K mutated primary leptomeningeal melanoma in a child: case presentation and discussion on clinical and diagnostic implications

G Angelino, MD De Pasquale, L De Sio, A Serra… - BMC cancer, 2016 - Springer
Background Primary melanocytic neoplasms are rare in the pediatric age. Among them, the
pattern of neoplastic meningitis represents a peculiar diagnostic challenge since …

Nevospheres from neurocutaneous melanocytosis cells show reduced viability when treated with specific inhibitors of NRAS signaling pathway

D Basu, CM Salgado, BS Bauer, D Johnson… - Neuro …, 2015 - academic.oup.com
Background Neurocutaneous melanocytosis (NCM) is characterized by clonal
nevomelanocytic proliferations in the CNS and skin. Given the scarcity of effective …

Severe hydrocephalus caused by diffuse leptomeningeal and neurocutaneous melanocytosis of antenatal onset: a clinical, pathologic, and molecular study of 2 cases

A Uguen, C Laurent, L Samaison, B Boisselier… - Human Pathology, 2015 - Elsevier
Diffuse leptomeningeal melanocytosis (DLM) is a rare nevomelanocytic proliferation arising
in the meninges. Despite their lack of morphological features of malignancy, these clonal …

Symptomatic neurocutaneous melanosis: mild clinical onset in a teenager

A Vanood, YA Lee, E Leleszi… - BMJ Case Reports …, 2020 - casereports.bmj.com
Neurocutaneous melanosis (NCM) is a rare disorder characterised by giant or multiple
melanocytic nevi and meningeal melanosis or melanoma. Onset of neurological symptoms …

Lin28A/let-7 oncogenic circuit is a potential therapeutic target in neurocutaneous melanosis-associated CNS tumors in children

M Jain, S Tran, S Thakur, Y Nagashima… - Neuro-Oncology …, 2021 - academic.oup.com
This study aims to describe the initial findings on the implication of Lin28A oncoprotein in
rare and currently difficult to cure CNS tumors associated with neurocutaneous melanosis in …

Insulin-like growth factor 1 receptor signaling via Akt: a general therapeutic target in neurocutaneous melanocytosis?

J Patel, CM Salgado, MR Múgica, D Basu - Neuro-oncology, 2015 - academic.oup.com
Symptomatic neurocutaneous melanocytosis (NCM) currently has no therapy and bears an
extremely poor prognosis. Although first described by Rokitansky in 1861, information on …