Regulation of ribosomal RNA gene copy number, transcription and nucleolus organization in eukaryotes

Y Hori, C Engel, T Kobayashi - Nature reviews Molecular cell biology, 2023 - nature.com
One of the first biological machineries to be created seems to have been the ribosome.
Since then, organisms have dedicated great efforts to optimize this apparatus. The …

Nucleolar stress: From development to cancer

MC Lafita-Navarro, M Conacci-Sorrell - Seminars in cell & developmental …, 2023 - Elsevier
The nucleolus is a large nuclear membraneless organelle responsible for ribosome
biogenesis. Ribosomes are cytoplasmic macromolecular complexes comprising RNA and …

Identification of rare and common regulatory variants in pluripotent cells using population-scale transcriptomics

MJ Bonder, C Smail, MJ Gloudemans, L Frésard… - Nature …, 2021 - nature.com
Induced pluripotent stem cells (iPSCs) are an established cellular system to study the impact
of genetic variants in derived cell types and developmental contexts. However, in their …

Genetic susceptibility loci in genomewide association study of cluster headache

AVE Harder, BS Winsvold, R Noordam… - Annals of …, 2021 - Wiley Online Library
Objective Identifying common genetic variants that confer genetic risk for cluster headache.
Methods We conducted a case–control study in the Dutch Leiden University Cluster …

RNA polymerases I and III in development and disease

KEN Watt, J Macintosh, G Bernard… - Seminars in cell & …, 2023 - Elsevier
Ribosomes are macromolecular machines that are globally required for the translation of all
proteins in all cells. Ribosome biogenesis, which is essential for cell growth, proliferation …

Cryo-EM structures of human RNA polymerase I

AD Misiaszek, M Girbig, H Grötsch, F Baudin… - Nature structural & …, 2021 - nature.com
Abstract RNA polymerase I (Pol I) specifically synthesizes ribosomal RNA. Pol I upregulation
is linked to cancer, while mutations in the Pol I machinery lead to developmental disorders …

Dynamic regulation and requirement for ribosomal RNA transcription during mammalian development

KT Falcon, KEN Watt, S Dash, R Zhao… - Proceedings of the …, 2022 - National Acad Sciences
Ribosomal RNA (rRNA) transcription by RNA polymerase I (Pol I) is a critical rate-limiting
step in ribosome biogenesis, which is essential for cell survival. Despite its global function …

A systematic review on Treacher Collins syndrome: Correlation between molecular genetic findings and clinical severity

ZS Ulhaq, DK Nurputra, GV Soraya… - Clinical …, 2023 - Wiley Online Library
Abstract Treacher Collins syndrome (TCS, OMIM: 154500) is a rare congenital craniofacial
disorder that is caused by variants in the genes TCOF1, POLR1D, POLR1C, and POLR1B …

How altered ribosome production can cause or contribute to human disease: the spectrum of ribosomopathies

G Venturi, L Montanaro - Cells, 2020 - mdpi.com
A number of different defects in the process of ribosome production can lead to a diversified
spectrum of disorders that are collectively identified as ribosomopathies. The specific factors …

rRNA transcription is integral to phase separation and maintenance of nucleolar structure

S Dash, MC Lamb, JJ Lange, MC McKinney… - PLoS …, 2023 - journals.plos.org
Transcription of ribosomal RNA (rRNA) by RNA Polymerase (Pol) I in the nucleolus is
necessary for ribosome biogenesis, which is intimately tied to cell growth and proliferation …