Auditory neuropathy—neural and synaptic mechanisms

T Moser, A Starr - Nature Reviews Neurology, 2016 - nature.com
Sensorineural hearing impairment is the most common form of hearing loss, and
encompasses pathologies of the cochlea and the auditory nerve. Hearing impairment …

Auditory synaptopathy, auditory neuropathy, and cochlear implantation

AE Shearer, MR Hansen - Laryngoscope investigative …, 2019 - Wiley Online Library
Cochlear implantation has become the standard‐of‐care for adults and children with severe
to profound hearing loss. There is growing evidence that qualitative as well as quantitative …

Multi-site diagnosis and management of 260 patients with Auditory Neuropathy/Dys-synchrony (Auditory Neuropathy Spectrum Disorder*)

CI Berlin, LJ Hood, T Morlet, D Wilensky… - … journal of audiology, 2010 - Taylor & Francis
Test results and management data are summarized for 260 patients with diagnoses of
Auditory Neuropathy Spectrum Disorder (ANSD). Hearing aids were tried in 85 of these …

Auditory neuropathy spectrum disorders: from diagnosis to treatment: literature review and case reports

RD De Siati, F Rosenzweig, G Gersdorff… - Journal of clinical …, 2020 - mdpi.com
Auditory neuropathy spectrum disorder (ANSD) refers to a range of hearing impairments
characterized by deteriorated speech perception, despite relatively preserved pure-tone …

[HTML][HTML] A proposal for comprehensive newborn hearing screening to improve identification of deaf and hard-of-hearing children

AE Shearer, J Shen, S Amr, CC Morton, RJ Smith - Genetics in Medicine, 2019 - Elsevier
Early intervention for newborns who are deaf or hard-of-hearing leads to improved
language, communication, and social–emotional outcomes. Universal physiologic newborn …

Impaired AIF-CHCHD4 interaction and mitochondrial calcium overload contribute to auditory neuropathy spectrum disorder in patient-iPSC-derived neurons with …

Y Qiu, H Wang, M Fan, H Pan, J Guan, Y Jiang… - Cell Death & …, 2023 - nature.com
Auditory neuropathy spectrum disorder (ANSD) is a hearing impairment caused by
dysfunction of inner hair cells, ribbon synapses, spiral ganglion neurons and/or the auditory …

Etiologic and audiologic evaluations after universal neonatal hearing screening: analysis of 170 referred neonates

F Declau, A Boudewyns, J Van den Ende… - …, 2008 - publications.aap.org
OBJECTIVE. The goal was to clarify the audiologic aspects and causes of congenital
hearing loss in children who failed universal neonatal hearing screening. METHODS. A …

The frequency of auditory neuropathy detected by universal newborn hearing screening program

G Kirkim, B Serbetcioglu, TK Erdag, K Ceryan - International journal of …, 2008 - Elsevier
OBJECTIVE: Auditory neuropathy/auditory dyssynchrony (AN/AD) has become a well-
accepted clinical entity. The combined use of oto-acoustic emissions (OAEs) and auditory …

ABR-based newborn hearing screening with MB11 BERAphone® using an optimized chirp for acoustical stimulation

M Cebulla, W Shehata-Dieler - International Journal of Pediatric …, 2012 - Elsevier
OBJECTIVE: At our center, the Maico MB11 BERAphone® device is used for newborn
hearing screening based on Auditory Brainstem Responses (ABR). In 2006, an optimized …

Prevalence and risk factors for auditory neuropathy spectrum disorder in a screened newborn population at risk for hearing loss

I Bielecki, A Horbulewicz, T Wolan - International journal of pediatric …, 2012 - Elsevier
OBJECTIVE: To determine the prevalence of Auditory Neuropathy Spectrum Disorder
(ANSD) among infants with sensorineural hearing loss (SNHL) and discuss the risk factors …