Abstract Aim The “2022 ACC/AHA Guideline for the Diagnosis and Management of Aortic
Disease” provides recommendations to guide clinicians in the diagnosis, genetic evaluation …

Poziom B Dane pochodzące z jednej randomizowanej próby klinicznej lub dużych badań
nierandomizowanych Poziom C Uzgodniona opinia ekspertów i/lub dane pochodzące z …

The aortic root is the predominant site for development of aneurysm caused by
heterozygous loss-of-function mutations in positive effectors of the transforming growth factor …

Marfan syndrome (MFS) is a disease in which connective tissue becomes weak secondary
to fibrillin-1 mutations, resulting in aortic dilatation, aneurysm formation, aortic dissection …

Abstract Aim The “2022 ACC/AHA Guideline for the Diagnosis and Management of Aortic
Disease” provides recommendations to guide clinicians in the diagnosis, genetic evaluation …

Background—Data on outcomes after Stanford type A aortic dissection in patients with
Marfan syndrome are limited. We investigated the primary surgery and long-term results in …

Objectives To define and compare growth rates of the distal aorta in Marfan patients with
and without aortic root replacement using serial MR angiography (MRA). Methods We …

Background In patients with Marfan syndrome (MFS), distal aortic dissection can necessitate
thoracoabdominal aortic aneurysm (TAAA) repair in survivors of acute DeBakey type I …

OBJECTIVES The aim of this study was to determine the outcome of Stanford type B aortic
dissection in patients with Marfan syndrome (MFS) and to evaluate aortic diameters at time …

OBJECTIVES Our goal was to evaluate the use of the frozen elephant trunk (FET) technique
for the treatment of penetrating aortic ulcers involving the aortic arch. METHODS Between …