Life expectancy and quality of life for those born with congenital heart disease (CHD) have
greatly improved over the past 3 decades. While representing a great advance for these …

Congenital portosystemic shunts are present in one in 30,000 children. Among the
associated risks of severe complications are neonatal cholestasis, benign and malignant …

Background Congenital portosystemic shunt (CPSS) is a rare malformation in which
splanchnic venous flow bypasses the liver. CPSS is associated with other congenital …

Congenital extrahepatic portosystemic shunt, also known as Abernethy malformation, is a
rare malformation in which intestinal and splenic venous blood bypasses the liver and …

Abernethy malformation, also known as congenital extrahepatic portosystemic shunts
(CEPS) is a rare clinical entity and manifests with different clinical symptoms. CEPS are …

Aim: Congenital extrahepatic portosystemic shunt (CEPS) is a rare anomaly in which the
enteric blood bypasses the liver and drains into the systemic veins through various venous …

In a review of 382 cases of congenital portosystemic shunt, we found that presentation with
neonatal cholestasis strongly predicts spontaneous closure of intrahepatic shunts (OR 8.3 …

Abernethy malformation is a rare congenital malformation defined by an extrahepatic
portosystemic shunt. The majority of affected patients are young (< 18 years of age) and …

Congenital portosystemic shunt (CPSS) is persistence of an anomalous embryological
connection of the portal vein with a large vein of the vena cava system. Clinical …

Objectives: Congenital portosystemic shunts (CPSS) are rare vascular malformations. We
describe presentations, complications, associations, and outcomes of CPSS at Boston …