The past 60 years have brought remarkable advancements in the diagnosis and treatment of
congenital heart disease (CHD). Early diagnosis and improvements in cardiac surgery and …

The Fontan procedure has led to increased long-term survival of patients with single
ventricle congenital heart disease. Hemodynamic changes associated with the Fontan …

Background: There are limited long-term, single-cohort, follow-up studies available about
patients after the Fontan operation. Objectives: This study sought to determine the long-term …

Background—The life expectancy of patients undergoing a Fontan procedure is unknown.
Methods and Results—Follow-up of all 1006 survivors of the 1089 patients who underwent a …

Life expectancy and quality of life for those born with congenital heart disease (CHD) have
greatly improved over the past 3 decades. While representing a great advance for these …

Background: Patients with protein-losing enteropathy (PLE) following the Fontan operation
have a reported 50% mortality at 5 years after diagnosis. Objectives: The aim of this study …

We reviewed records of all patients with an initial Fontan operation or revision from 1973 to
2012 at our institution (n= 1,138); 195 patients had postoperative liver data available …

Objectives Liver disease is an important contributor to morbidity and mortality in patients
after Fontan surgery. There has been no large-scale survey of liver health in this population …

Fontan-associated liver disease (FALD) is a form of congestive hepatopathy that is universal
among patients who have undergone Fontan palliation for functional single ventricle …

Fontan-associated liver disease is a hepatic disorder arising from hemodynamic changes
and systemic venous congestion following Fontan surgery. The histological changes …