Opportunities, barriers, and recommendations in Down syndrome research

JA Hendrix, A Amon, L Abbeduto… - … science of rare …, 2021 - journals.sagepub.com
BACKGROUND: Recent advances in medical care have increased life expectancy and
improved the quality of life for people with Down syndrome (DS). These advances are the …

New approaches to studying early brain development in Down syndrome

AA Baburamani, PA Patkee, T Arichi… - … medicine & child …, 2019 - Wiley Online Library
Down syndrome is the most common genetic developmental disorder in humans and is
caused by partial or complete triplication of human chromosome 21 (trisomy 21). It is a …

Trisomy 21 consistently activates the interferon response

KD Sullivan, HC Lewis, AA Hill, A Pandey, LP Jackson… - Elife, 2016 - elifesciences.org
Although it is clear that trisomy 21 causes Down syndrome, the molecular events acting
downstream of the trisomy remain ill defined. Using complementary genomics analyses, we …

Safety and efficacy of cognitive training plus epigallocatechin-3-gallate in young adults with Down's syndrome (TESDAD): a double-blind, randomised, placebo …

R de la Torre, S de Sola, G Hernandez, M Farré… - The Lancet …, 2016 - thelancet.com
Background Early cognitive intervention is the only routine therapeutic approach used for
amelioration of intellectual deficits in individuals with Down's syndrome, but its effects are …

Association of dementia with mortality among adults with Down syndrome older than 35 years

R Hithersay, CM Startin, S Hamburg, KY Mok… - JAMA …, 2019 - jamanetwork.com
Importance This work quantifies the fatal burden of dementia associated with Alzheimer
disease in individuals with Down syndrome (DS). Objective To explore the association of …

Outcome measures for clinical trials in Down syndrome

AJ Esbensen, SR Hooper, D Fidler… - … on intellectual and …, 2017 - meridian.allenpress.com
Increasingly individuals with intellectual and developmental disabilities, including Down
syndrome, are being targeted for clinical trials. However, a challenge exists in effectively …

Trisomy 21 activates the kynurenine pathway via increased dosage of interferon receptors

RK Powers, R Culp-Hill, MP Ludwig, KP Smith… - Nature …, 2019 - nature.com
Abstract Trisomy 21 (T21) causes Down syndrome (DS), affecting immune and neurological
function by ill-defined mechanisms. Here we report a large metabolomics study of plasma …

Adaptive behaviour, executive function and employment in adults with Down syndrome

B Tomaszewski, D Fidler, D Talapatra… - Journal of Intellectual …, 2018 - Wiley Online Library
Abstract Background Individuals with Down syndrome (DS) demonstrate difficulties with
aspects of executive function (EF) and adaptive behaviour across the lifespan. There is a …

Assessment of cognitive scales to examine memory, executive function and language in individuals with Down syndrome: implications of a 6-month observational …

X Liogier d'Ardhuy, JO Edgin, C Bouis… - Frontiers in Behavioral …, 2015 - frontiersin.org
Down syndrome (DS) is the most commonly identifiable genetic form of intellectual disability.
Individuals with DS have considerable deficits in intellectual functioning (ie, low intellectual …

Cognitive decline and dementia in Down syndrome

R Hithersay, S Hamburg, B Knight… - Current opinion in …, 2017 - journals.lww.com
Clinical trials of treatments, particularly in the presymptomatic phase of Alzheimer's disease,
are important to consider in individuals with Down syndrome given their high dementia …