Myotonic dystrophy type 1 (DM1), the most common muscular dystrophy affecting adults and
children, is a multi-systemic disorder affecting skeletal, cardiac, and smooth muscles as well …

Myotonic dystrophy is a hereditary disorder with systemic involvement. The Italian Neuro-
Cardiology Network-“Rete delle Neurocardiologie”(INCN-RNC) is a unique collaborative …

Objectives In patients with advanced liver disease, portal hypertension is an important risk
factor, leading to complications such as esophageal variceal bleeding, ascites, and hepatic …

Abstract Purpose of Review This review aims to outline the utility of cardiac magnetic
resonance (CMR) in patients with different types of muscular dystrophies for the assessment …

Muscular dystrophies are inherited disorders sharing similar clinical features and dystrophic
changes on muscle biopsy. Duchenne muscular dystrophy is the most common inherited …

Background Myocardial native T1 and T2 relaxation time mapping are sensitive to
pathological increase of myocardial water content (eg myocardial edema). However, the …

Purpose of Review: Left ventricular arrhythmogenic cardiomyopathy (ALVC) is a rare and
poorly characterized cardiomyopathy that has recently been reclassified in the group of non …

Background Myotonic dystrophy type 1 (DM1) is a multisystemic disorder characterized by
progressive cardiac conduction impairment, arrhythmias, and sudden death. Mexiletine is a …

Muscular dystrophies (MD) represent a heterogeneous group of rare genetic diseases that
often lead to significant weakness due to progressive muscle degeneration. In many forms of …

Introduction: To evaluate myocardial strain and extracellular volume in myotonic dystrophy
type 1 (DM1) patients as potential imaging biomarkers of subclinical cardiac pathology …