microRNA dysregulation in neurodegenerative diseases: A systematic review

CA Juźwik, SS Drake, Y Zhang, N Paradis-Isler… - Progress in …, 2019 - Elsevier
While the root causes for individual neurodegenerative diseases are distinct, many shared
pathological features and mechanisms contribute to neurodegeneration across diseases …

Dysregulated molecular pathways in amyotrophic lateral sclerosis–frontotemporal dementia spectrum disorder

FB Gao, S Almeida, R Lopez‐Gonzalez - The EMBO journal, 2017 - embopress.org
Frontotemporal dementia (FTD), the second most common form of dementia in people under
65 years of age, is characterized by progressive atrophy of the frontal and/or temporal lobes …

Poly (GR) in C9ORF72-related ALS/FTD compromises mitochondrial function and increases oxidative stress and DNA damage in iPSC-derived motor neurons

R Lopez-Gonzalez, Y Lu, TF Gendron, A Karydas… - Neuron, 2016 - cell.com
GGGGCC repeat expansions in C9ORF72 are the most common genetic cause of both ALS
and FTD. To uncover underlying pathogenic mechanisms, we found that DNA damage was …

C9ORF72-ALS/FTD-associated poly (GR) binds Atp5a1 and compromises mitochondrial function in vivo

SY Choi, R Lopez-Gonzalez, G Krishnan… - Nature …, 2019 - nature.com
The GGGGCC repeat expansion in C9ORF72 is the most common genetic cause of
amyotrophic lateral sclerosis (ALS) and frontotemporal dementia (FTD). However, it is not …

Human C9ORF72 hexanucleotide expansion reproduces RNA foci and dipeptide repeat proteins but not neurodegeneration in BAC transgenic mice

OM Peters, GT Cabrera, H Tran, TF Gendron… - Neuron, 2015 - cell.com
A non-coding hexanucleotide repeat expansion in the C9ORF72 gene is the most common
mutation associated with familial amyotrophic lateral sclerosis (ALS) and frontotemporal …

C9ORF72 repeat expansion causes vulnerability of motor neurons to Ca2+-permeable AMPA receptor-mediated excitotoxicity

BT Selvaraj, MR Livesey, C Zhao, JM Gregory… - Nature …, 2018 - nature.com
Mutations in C9ORF72 are the most common cause of familial amyotrophic lateral sclerosis
(ALS). Here, through a combination of RNA-Seq and electrophysiological studies on …

The promise of microRNA-based therapies in Alzheimer's disease: challenges and perspectives

H Walgrave, L Zhou, B De Strooper, E Salta - Molecular …, 2021 - Springer
Multi-pathway approaches for the treatment of complex polygenic disorders are emerging as
alternatives to classical monotarget therapies and microRNAs are of particular interest in …

Dysregulated mi RNA biogenesis downstream of cellular stress and ALS‐causing mutations: a new mechanism for ALS

A Emde, C Eitan, LL Liou, RT Libby, N Rivkin… - The EMBO …, 2015 - embopress.org
Interest in RNA dysfunction in amyotrophic lateral sclerosis (ALS) recently aroused upon
discovering causative mutations in RNA‐binding protein genes. Here, we show that …

Identification of microRNA-124-3p as a putative epigenetic signature of major depressive disorder

B Roy, M Dunbar, RC Shelton, Y Dwivedi - Neuropsychopharmacology, 2017 - nature.com
Major depressive disorder (MDD) is predicted to be the second leading cause of global
disease burden by 2030. A large number of MDD patients do not respond to the currently …

Neurotransmitter deficits from frontotemporal lobar degeneration

AG Murley, JB Rowe - Brain, 2018 - academic.oup.com
Frontotemporal lobar degeneration causes a spectrum of complex degenerative disorders
including frontotemporal dementia, progressive supranuclear palsy and corticobasal …