Hypoplastic left heart syndrome: current considerations and expectations

JA Feinstein, DW Benson, AM Dubin, MS Cohen… - Journal of the American …, 2012 - jacc.org
In the recent era, no congenital heart defect has undergone a more dramatic change in
diagnostic approach, management, and outcomes than hypoplastic left heart syndrome …

The Fontan circulation: who controls cardiac output?

M Gewillig, SC Brown, B Eyskens… - … and thoracic surgery, 2010 - academic.oup.com
In a Fontan circuit the mechanisms involved in control of cardiac output at rest and during
exercise differ significantly from normal. The classical model presumes an unlimited preload …

Four decades of Fontan palliation

MR De Leval, JE Deanfield - Nature Reviews Cardiology, 2010 - nature.com
The Fontan palliation was introduced in 1968 to treat cardiac malformations unsuitable for
biventricular repair. This procedure has transformed the surgical management of congenital …

Fontan‐associated liver disease

MB Hilscher, ML Wells, SK Venkatesh, F Cetta… - Hepatology, 2022 - journals.lww.com
Fontan‐associated liver disease : Hepatology Fontan‐associated liver disease : Hepatology
AASLD Publications Hepatology Liver Transplantation Clinical Liver Disease Hepatology …

Transplantation and mechanical circulatory support in congenital heart disease: a scientific statement from the American Heart Association

HJ Ross, Y Law, WM Book, CS Broberg, L Burchill… - Circulation, 2016 - Am Heart Assoc
Ross et al Transplantation in Congenital Heart Disease 803 listed ACHD patients are more
likely to experience cardiovascular death (including sudden death and death caused by HF) …

The Fontan circulation: a challenge to William Harvey?

MR De Leval - Nature clinical practice Cardiovascular medicine, 2005 - nature.com
The Fontan operation, which places the systemic and pulmonary circulations in series and is
driven by a single ventricular chamber, is the treatment of choice for patients born with one …

[PDF][PDF] Increased hepatic stiffness as consequence of high hepatic afterload in the Fontan circulation: a vascular Doppler and elastography study

SS Kutty, Q Peng, DA Danford, SE Fletcher… - …, 2014 - Wiley Online Library
Hepatic dysfunction is a recognized complication after Fontan palliation of congenital heart
disease. We sought to quantitatively measure hepatic stiffness and vascular Doppler indices …

Liver disease in the patient with Fontan circulation

FM Wu, C Ukomadu, RD Odze… - Congenital heart …, 2011 - Wiley Online Library
The Fontan procedure has undergone many modifications since first being performed on a
patient with tricuspid valve atresia in 1968. It is now the procedure of choice for individuals …

Extracorporeal membrane oxygenation support of the Fontan and bidirectional Glenn circulations

KL Booth, SJ Roth, RR Thiagarajan… - The Annals of thoracic …, 2004 - Elsevier
BACKGROUND: Extracorporeal membrane oxygenation can provide effective mechanical
circulatory support for the failing circulation in children. Patients with failing Fontan and …

[HTML][HTML] The influence of respiration on blood flow in the Fontan circulation: insights for imaging-based clinical evaluation of the total cavopulmonary connection

SLFS Van der Woude, FM Rijnberg… - Frontiers in …, 2021 - frontiersin.org
Congenital heart disease is the most common birth defect and functionally univentricular
heart defects represent the most severe end of this spectrum. The Fontan circulation …