Usher syndrome (USH) is the most common genetic condition responsible for combined loss
of hearing and vision. Balance disorders and bilateral vestibular areflexia are also observed …

Importance In 2019, the US Food and Drug Administration approved cochlear implantation
for children with single-sided deafness (SSD). The absence of robust clinical data specific to …

This article summarizes the available evidence on pediatric cochlear implantation to provide
current guidelines for clinical protocols and candidacy recommendations in the United …

Objective: Incomplete partition type 3 (IP3) malformation deafness is a rare hereditary cause
of congenital or rapid progressive hearing loss. The children present with a severe to …

Solute carrier family 26 member 4 (SLC26A4) is a member of the SLC26A transporter family
and is expressed in various tissues, including the airway epithelium, kidney, thyroid, and …

Background Identifying predictive factors of the cochlear implant outcomes in pediatric
patients is critical in guiding tailored rehabilitation programs. The study aimed to assess …

Pendred syndrome (PDS) is the most common form of syndromic Hearing Loss (HL),
characterized by sensorineural HL, inner ear malformations, and goiter, with or without …

Usher syndrome (US) is a clinically and genetically heterogeneous disorder that involves
three main features: sensorineural hearing loss, retinitis pigmentosa (RP), and vestibular …

Objectives: This study investigated age at implantation, improvement in hearing and speech
perception outcomes, as well as surgical complications in pediatric cochlear implant …

Objectives: Patients with X-linked incomplete partition type III (IP3) deafness treated with
cochlear implants exhibit higher “Most Comfortable Loudness”(MCL) levels of stimulation …