Molecular mechanism of nucleotide excision repair

WL de Laat, NGJ Jaspers… - Genes & …, 1999 - genesdev.cshlp.org
From its very beginning, life has faced the fundamental problem that the form in which
genetic information is stored is not chemically inert. DNA integrity is challenged by the …

Mechanisms of interstrand DNA crosslink repair and human disorders

S Hashimoto, H Anai, K Hanada - Genes and Environment, 2016 - Springer
Interstrand DNA crosslinks (ICLs) are the link between Watson-Crick strands of DNAs with
the covalent bond and prevent separation of DNA strands. Since the ICL lesion affects both …

[图书][B] DNA repair and mutagenesis

EC Friedberg, GC Walker, W Siede, RD Wood - 2005 - books.google.com
An essential resource for all scientists researching cellular responses to DNA damage.•
Introduces important new material reflective of the major changes and developments that …

Sequence Variants in SLITRK1 Are Associated with Tourette's Syndrome

JF Abelson, KY Kwan, BJ O'Roak, DY Baek… - Science, 2005 - science.org
Tourette's syndrome (TS) is a genetically influenced developmental neuropsychiatric
disorder characterized by chronic vocal and motor tics. We studied Slit and Trk-like 1 …

[HTML][HTML] Mechanism of open complex and dual incision formation by human nucleotide excision repair factors

E Evans, JG Moggs, JR Hwang, JM Egly… - The EMBO …, 1997 - embopress.org
During nucleotide excision repair in human cells, a damaged DNA strand is cleaved by two
endonucleases, XPG on the 3′ side of the lesion and ERCC1‐XPF on the 5′ side. These …

Deep phenotyping of 89 xeroderma pigmentosum patients reveals unexpected heterogeneity dependent on the precise molecular defect

H Fassihi, M Sethi, H Fawcett, J Wing… - Proceedings of the …, 2016 - National Acad Sciences
Xeroderma pigmentosum (XP) is a rare DNA repair disorder characterized by increased
susceptibility to UV radiation (UVR)-induced skin pigmentation, skin cancers, ocular surface …

Base excision repair of oxidative DNA damage activated by XPG protein

A Klungland, M Höss, D Gunz, A Constantinou… - Molecular cell, 1999 - cell.com
Oxidized pyrimidines in DNA are removed by a distinct base excision repair pathway
initiated by the DNA glycosylase—AP lyase hNth1 in human cells. We have reconstituted …

XPG stabilizes TFIIH, allowing transactivation of nuclear receptors: implications for Cockayne syndrome in XP-G/CS patients

S Ito, I Kuraoka, P Chymkowitch, E Compe… - Molecular cell, 2007 - cell.com
Mutations in the human XPG gene give rise to an inherited photosensitive disorder,
xeroderma pigmentosum (XP) associated with Cockayne syndrome (XP-G/CS). The clinical …

Nucleotide excision repair and cancer

D Leibeling, P Laspe, S Emmert - Journal of molecular histology, 2006 - Springer
Nucleotide excision repair (NER) is the most versatile and best studied DNA repair system in
humans. NER can repair a variety of bulky DNA damages including UV-light induced DNA …

Defective transcription-coupled repair of oxidative base damage in Cockayne syndrome patients from XP group G

PK Cooper, T Nouspikel, SG Clarkson, SA Leadon - Science, 1997 - science.org
In normal human cells, damage due to ultraviolet light is preferentially removed from active
genes by nucleotide excision repair (NER) in a transcription-coupled repair (TCR) process …