Pulmonary hypertension

A Mocumbi, M Humbert, A Saxena, ZC Jing… - Nature Reviews …, 2024 - nature.com
Pulmonary hypertension encompasses a range of conditions directly or indirectly leading to
elevated pressures within the pulmonary arteries. Five main groups of pulmonary …

Pulmonary arterial hypertension: pathogenesis and clinical management

T Thenappan, ML Ormiston, JJ Ryan, SL Archer - Bmj, 2018 - bmj.com
Pulmonary hypertension is defined as a resting mean pulmonary artery pressure of 25 mm
Hg or above. This review deals with pulmonary arterial hypertension (PAH), a type of …

Assessment of right ventricular function in the research setting: knowledge gaps and pathways forward. An Official American Thoracic Society Research Statement

T Lahm, IS Douglas, SL Archer, HJ Bogaard… - American journal of …, 2018 - atsjournals.org
Background: Right ventricular (RV) adaptation to acute and chronic pulmonary hypertensive
syndromes is a significant determinant of short-and long-term outcomes. Although …

The right ventricle in pulmonary arterial hypertension: disorders of metabolism, angiogenesis and adrenergic signaling in right ventricular failure

JJ Ryan, SL Archer - Circulation research, 2014 - Am Heart Assoc
The right ventricle (RV) is the major determinant of functional state and prognosis in
pulmonary arterial hypertension. RV hypertrophy (RVH) triggered by pressure overload is …

Metabolism in pulmonary hypertension

W Xu, AJ Janocha, SC Erzurum - Annual review of physiology, 2021 - annualreviews.org
Pulmonary arterial hypertension (PAH) is characterized by impaired regulation of pulmonary
hemodynamics and vascular growth. Alterations of metabolism and bioenergetics are …

Cardiac fibrosis in the pressure overloaded left and right ventricle as a therapeutic target

K Schimmel, K Ichimura, S Reddy, F Haddad… - Frontiers in …, 2022 - frontiersin.org
Myocardial fibrosis is a remodeling process of the extracellular matrix (ECM) following
cardiac stress.“Replacement fibrosis” is a term used to describe wound healing in the acute …

Identification of microRNA-124 as a major regulator of enhanced endothelial cell glycolysis in pulmonary arterial hypertension via PTBP1 (polypyrimidine tract binding …

P Caruso, BJ Dunmore, K Schlosser, S Schoors… - Circulation, 2017 - Am Heart Assoc
Background: Pulmonary arterial hypertension (PAH) is characterized by abnormal growth
and enhanced glycolysis of pulmonary artery endothelial cells. However, the mechanisms …

[HTML][HTML] Dynamin-related protein 1 (Drp1)-mediated diastolic dysfunction in myocardial ischemia-reperfusion injury: therapeutic benefits of Drp1 inhibition to reduce …

WW Sharp, YH Fang, M Han, HJ Zhang, Z Hong… - The FASEB …, 2014 - ncbi.nlm.nih.gov
Mitochondrial fission, regulated by dynamin-related protein-1 (Drp1), is a newly recognized
determinant of mitochondrial function, but its contribution to left ventricular (LV) impairment …

Fatty acid metabolic defects and right ventricular lipotoxicity in human pulmonary arterial hypertension

EL Brittain, M Talati, JP Fessel, H Zhu, N Penner… - Circulation, 2016 - Am Heart Assoc
Background—The mechanisms of right ventricular (RV) failure in pulmonary arterial
hypertension (PAH) are poorly understood. Abnormalities in fatty acid (FA) metabolism have …

BMPR2 Mutation and Metabolic Reprogramming in Pulmonary Arterial Hypertension

I Cuthbertson, NW Morrell, P Caruso - Circulation research, 2023 - Am Heart Assoc
Pulmonary arterial hypertension forms the first and most severe of the 5 categories of
pulmonary hypertension. Disease pathogenesis is driven by progressive remodeling of …