Fontan-associated liver disease: screening, management, and transplant considerations

J Emamaullee, AN Zaidi, T Schiano, J Kahn… - Circulation, 2020 - Am Heart Assoc
Surgical innovation and multidisciplinary management have allowed children born with
univentricular physiology congenital heart disease to survive into adulthood. An estimated …

[PDF][PDF] Biliary atresia in children: update on disease mechanism, therapies, and patient outcomes

S Antala, SA Taylor - Clinics in liver disease, 2022 - Elsevier
Biliary atresia is a rare disease but remains the most common indication for pediatric liver
transplantation as there are no effective medical therapies to slow progression after …

Biliary atresia: Potential for a new decade

F Scottoni, M Davenport - Seminars in Pediatric Surgery, 2020 - Elsevier
Biliary atresia is characterised as an obliterative cholangiopathy of both extra-and intra-
hepatic bile ducts. There is marked aetiological heterogeneity with a number of different …

Primary vs. salvage liver transplantation for biliary atresia: A retrospective cohort study

D Yoeli, RA Choudhury, SS Sundaram, CL Mack… - Journal of pediatric …, 2022 - Elsevier
Introduction Kasai hepatoportoenterostomy is the standard of care for children with biliary
atresia, but a majority of patients progress to end-stage liver disease and require a salvage …

The outcome of a centralization program in biliary atresia: 20 years and beyond

M Davenport, E Makin, EGP Ong, K Sharif… - Annals of …, 2024 - journals.lww.com
Objective: Biliary atresia (BA) is a rare disease and reported outcomes of surgical
management, typically a Kasai portoenterostomy (KPE), vary considerably across the world …

Sequential treatment of biliary atresia with Kasai hepatoportoenterostomy and liver transplantation: benefits, risks, and outcome in 393 children

R Tambucci, C De Magnee, M Szabo… - Frontiers in …, 2021 - frontiersin.org
Introduction: Surgical treatment of biliary atresia (BA) is still based on sequential strategy
with Kasai hepatoportoenterostomy (KP) followed by liver transplantation (LT), in case of …

Improved outcomes for liver transplantation in patients with biliary atresia since pediatric end-stage liver disease implementation: analysis of the society of pediatric …

SA Taylor, V Venkat, R Arnon, VV Gopalareddy… - The Journal of …, 2020 - Elsevier
Objective To identify changes in demographics, outcomes, and risk factors for patient and
graft loss in patients with biliary atresia undergoing liver transplantation since Pediatric End …

Primary liver transplantation vs. transplant after Kasai portoenterostomy for infants with biliary atresia

CP Lemoine, JP LeShock, KA Brandt… - Journal of clinical …, 2022 - mdpi.com
Introduction: Primary liver transplants (pLT) in patients with biliary atresia (BA) are
infrequent, since most babies with BA undergo a prior Kasai portoenterostomy (KPE). This …

Early life growth and developmental trajectory in children with biliary atresia undergoing primary liver transplantation

H Fang, Z Li, R Xian, Y Yin, J Wang, H Guo… - Frontiers in …, 2023 - frontiersin.org
Objective To clarify the early growth and developmental characteristics of children with
biliary atresia (BA) undergoing primary liver transplantation (pLT). Methods A prospective …

Impact of the Kasai procedure and the length of native liver survival time on outcomes of liver transplantation for biliary atresia

L Liu, L Wei, W Qu, Y Liu, Z Zeng, H Zhang… - Liver …, 2022 - Wiley Online Library
The aim is to explore the impact of the Kasai procedure (KP) and the length of native liver
survival time (NLST) on outcomes of liver transplantation (LT). Patients with biliary atresia …