Insights into genetics, human biology and disease gleaned from family based genomic studies

JE Posey, AH O'Donnell-Luria, JX Chong, T Harel… - Genetics in …, 2019 - nature.com
Identifying genes and variants contributing to rare disease phenotypes and Mendelian
conditions informs biology and medicine, yet potential phenotypic consequences for …

Clinical genetics of spondylocostal dysostosis: A mini review

M Umair, M Younus, S Shafiq, A Nayab… - Frontiers in …, 2022 - frontiersin.org
Spondylocostal dysostosis is a genetic defect associated with severe rib and vertebrae
malformations. In recent years, extensive clinical and molecular diagnosis advancements …

Clan genomics: From OMIM phenotypic traits to genes and biology

JR Lupski - American Journal of Medical Genetics Part A, 2021 - Wiley Online Library
Clinical characterization of a patient phenotype has been the quintessential approach for
elucidating a differential diagnosis and a hypothesis to explore a potential clinical diagnosis …

Prenatal diagnosis of fetuses with increased nuchal translucency by genome sequencing analysis

KW Choy, H Wang, M Shi, J Chen, Z Yang… - Frontiers in …, 2019 - frontiersin.org
Background: Increased nuchal translucency (NT) is an important biomarker associated with
increased risk of fetal structural anomalies. It is known to be contributed by a wide range of …

Perturbations of genes essential for Müllerian duct and Wölffian duct development in Mayer-Rokitansky-Küster-Hauser syndrome

N Chen, S Zhao, A Jolly, L Wang, H Pan, J Yuan… - The American Journal of …, 2021 - cell.com
Mayer-Rokitansky-Küster-Hauser syndrome (MRKHS) is associated with congenital
absence of the uterus, cervix, and the upper part of the vagina; it is a sex-limited trait …

COL11A2 as a candidate gene for vertebral malformations and congenital scoliosis

D Rebello, E Wohler, V Erfani, G Li… - Human molecular …, 2023 - academic.oup.com
Human vertebral malformations (VMs) have an estimated incidence of 1/2000 and are
associated with significant health problems including congenital scoliosis (CS) and recurrent …

Unraveling the genetic architecture of congenital vertebral malformation with reference to the developing spine

S Zhao, H Zhao, L Zhao, X Cheng, Z Zheng… - Nature …, 2024 - nature.com
Abstract Congenital vertebral malformation, affecting 0.13–0.50 per 1000 live births, has an
immense locus heterogeneity and complex genetic architecture. In this study, we analyze …

Diagnostic yield and clinical impact of exome sequencing in early-onset scoliosis (EOS)

S Zhao, Y Zhang, W Chen, W Li, S Wang… - Journal of medical …, 2021 - jmg.bmj.com
Background Early-onset scoliosis (EOS), defined by an onset age of scoliosis less than 10
years, conveys significant health risk to affected children. Identification of the molecular …

The pleiotropic spectrum of proximal 16p11. 2 CNVs

C Auwerx, Z Kutalik, A Reymond - The American Journal of Human …, 2024 - cell.com
Recurrent genomic rearrangements at 16p11. 2 BP4-5 represent one of the most common
causes of genomic disorders. Originally associated with increased risk for autism spectrum …

A genocentric approach to discovery of Mendelian disorders

AW Hansen, M Murugan, H Li, MM Khayat… - The American Journal of …, 2019 - cell.com
The advent of inexpensive, clinical exome sequencing (ES) has led to the accumulation of
genetic data from thousands of samples from individuals affected with a wide range of …