Gene therapy for human sensorineural hearing loss

Y Ren, LD Landegger, KM Stankovic - Frontiers in Cellular …, 2019 - frontiersin.org
Hearing loss is the most common sensory impairment in humans and currently disables 466
million people across the world. Congenital deafness affects at least 1 in 500 newborns, and …

On the Role of Fibrocytes and the Extracellular Matrix in the Physiology and Pathophysiology of the Spiral Ligament

N Peeleman, D Verdoodt, P Ponsaerts… - Frontiers in …, 2020 - frontiersin.org
The spiral ligament in the cochlea has been suggested to play a significant role in the
pathophysiology of different etiologies of strial hearing loss. Spiral ligament fibrocytes …

Three-dimensional tonotopic mapping of the human cochlea based on synchrotron radiation phase-contrast imaging

H Li, L Helpard, J Ekeroot, SA Rohani, N Zhu… - Scientific reports, 2021 - nature.com
The human cochlea transforms sound waves into electrical signals in the acoustic nerve
fibers with high acuity. This transformation occurs via vibrating anisotropic membranes …

An approach for individualized cochlear frequency mapping determined from 3D synchrotron radiation phase-contrast imaging

L Helpard, H Li, SA Rohani, N Zhu… - IEEE Transactions …, 2021 - ieeexplore.ieee.org
Objective: Cochlear implants are traditionally programmed to stimulate according to a
generalized frequency map, where individual anatomic variability is not considered when …

Synchrotron radiation-based reconstruction of the human spiral ganglion: implications for cochlear implantation

H Li, N Schart-Moren, SA Rohani, HM Ladak… - Ear and …, 2020 - journals.lww.com
Objective: To three-dimensionally reconstruct Rosenthal's canal (RC) housing the human
spiral ganglion (SG) using synchrotron radiation phase-contrast imaging (SR-PCI). Straight …

Cytokine levels in inner ear fluid of young and aged mice as molecular biomarkers of noise-induced hearing loss

LD Landegger, S Vasilijic, T Fujita, VY Soares… - Frontiers in …, 2019 - frontiersin.org
Sensorineural hearing loss (SNHL) is the most common sensory deficit worldwide,
frequently caused by noise trauma and aging, with inflammation being implicated in both …

The panoramic ECAP method: estimating patient-specific patterns of current spread and neural health in cochlear implant users

C Garcia, T Goehring, S Cosentino, RE Turner… - Journal of the …, 2021 - Springer
The knowledge of patient-specific neural excitation patterns from cochlear implants (CIs) can
provide important information for optimizing efficacy and improving speech perception …

Characterization of the human helicotrema: implications for cochlear duct length and frequency mapping

L Helpard, H Li, H Rask-Andersen… - … -Head & Neck …, 2020 - journals.sagepub.com
Background Despite significant anatomical variation amongst patients, cochlear implant
frequency-mapping has traditionally followed a patient-independent approach. Basilar …

Cochlear histopathology in human genetic hearing loss: state of the science and future prospects

K Bommakanti, JS Iyer, KM Stankovic - Hearing research, 2019 - Elsevier
Sensorineural hearing loss (SNHL) is an extraordinarily common disability, affecting 466
million people across the globe. Half of these incidents are attributed to genetic mutations …

Adeno-associated virus gene replacement for recessive inner ear dysfunction: Progress and challenges

C Askew, WW Chien - Hearing research, 2020 - Elsevier
Approximately 3 in 1000 children in the US under 4 years of age are affected by hearing
loss. Currently, cochlear implants represent the only line of treatment for patients with severe …