A critical review of white matter changes in Huntington's disease

C Casella, I Lipp, A Rosser, DK Jones… - Movement …, 2020 - Wiley Online Library
Huntington's disease is a genetic neurodegenerative disorder. White matter alterations have
recently been identified as a relevant pathophysiological feature of Huntington's disease, but …

[HTML][HTML] Cell-autonomous and non-cell-autonomous pathogenic mechanisms in Huntington's disease: insights from in vitro and in vivo models

J Creus-Muncunill, ME Ehrlich - Neurotherapeutics, 2019 - Elsevier
Huntington's disease (HD) is an autosomal dominant disorder caused by an expansion in
the trinucleotide CAG repeat in exon-1 in the huntingtin gene, located on chromosome 4 …

Insights into white matter defect in Huntington's disease

Y Sun, H Tong, T Yang, L Liu, XJ Li, S Li - Cells, 2022 - mdpi.com
Huntington's disease (HD) is an autosomal-dominant inherited progressive
neurodegenerative disorder. It is caused by a CAG repeat expansion in the Huntingtin gene …

Combination of stem cell and gene therapy ameliorates symptoms in Huntington's disease mice

IK Cho, CE Hunter, S Ye, AL Pongos… - NPJ Regenerative …, 2019 - nature.com
Huntington's disease (HD) is a dominantly inherited monogenetic disorder characterized by
motor and cognitive dysfunction due to neurodegeneration. The disease is caused by the …

A molecular and cellular perspective on human brain evolution and tempo

FW Lindhout, FM Krienen, KS Pollard, MA Lancaster - Nature, 2024 - nature.com
The evolution of the modern human brain was accompanied by distinct molecular and
cellular specializations, which underpin our diverse cognitive abilities but also increase our …

A biocompatible and injectable hydrogel to boost the efficacy of stem cells in neurodegenerative diseases treatment

H Ferreira, D Amorim, AC Lima, RP Pirraco… - Life Sciences, 2021 - Elsevier
Aims Stem cell therapies emerged as treatment modalities with potential to cure
neurodegenerative diseases (NDs). However, despite high expectations, their clinical use is …

Large animal models of Huntington's disease: what we have learned and where we need to go next

D Howland, Z Ellederova, N Aronin… - Journal of …, 2020 - content.iospress.com
Genetically modified rodent models of Huntington's disease (HD) have been especially
valuable to our understanding of HD pathology and the mechanisms by which the mutant …

Amelioration of Huntington's disease phenotype in astrocytes derived from iPSC-derived neural progenitor cells of Huntington's disease monkeys

IK Cho, B Yang, C Forest, L Qian, AWS Chan - PLoS One, 2019 - journals.plos.org
Huntington's disease (HD) is a devastating monogenic, dominant, hereditary,
neurodegenerative disease. HD is caused by the expansion of CAG repeats in exon 1 of the …

A novel rhesus macaque model of Huntington's disease recapitulates key neuropathological changes along with motor and cognitive decline

AR Weiss, WA Liguore, K Brandon, X Wang, Z Liu… - Elife, 2022 - elifesciences.org
We created a new nonhuman primate model of the genetic neurodegenerative disorder
Huntington's disease (HD) by injecting a mixture of recombinant adeno-associated viral …

Infantile iron deficiency affects brain development in monkeys even after treatment of anemia

RM Vlasova, Q Wang, A Willette, MA Styner… - Frontiers in Human …, 2021 - frontiersin.org
A high percent of oxidative energy metabolism is needed to support brain growth during
infancy. Unhealthy diets and limited nutrition, as well as other environmental insults, can …