Myasthenia gravis: pathogenic effects of autoantibodies on neuromuscular architecture

I Koneczny, R Herbst - Cells, 2019 - mdpi.com
Myasthenia gravis (MG) is an autoimmune disease of the neuromuscular junction (NMJ).
Autoantibodies target key molecules at the NMJ, such as the nicotinic acetylcholine receptor …

Anti-inflammatory and neuroprotective agents in clinical trials for CNS disease and injury: where do we go from here?

K Mallah, C Couch, DM Borucki, A Toutonji… - Frontiers in …, 2020 - frontiersin.org
Neurological disorders are major contributors to death and disability worldwide. The
pathology of injuries and disease processes includes a cascade of events that often involve …

Terminal complement pathway activation drives synaptic loss in Alzheimer's disease models

SM Carpanini, M Torvell, RJ Bevan, RAJ Byrne… - Acta Neuropathologica …, 2022 - Springer
Complement is involved in developmental synaptic pruning and pathological synapse loss
in Alzheimer's disease. It is posited that C1 binding initiates complement activation on …

Broadly effective metabolic and immune recovery with C5 inhibition in CHAPLE disease

A Ozen, N Kasap, I Vujkovic-Cvijin, R Apps… - Nature …, 2021 - nature.com
Complement hyperactivation, angiopathic thrombosis and protein-losing enteropathy
(CHAPLE disease) is a lethal disease caused by genetic loss of the complement regulatory …

Clinical efficacy and safety of eculizumab for treating myasthenia gravis

H Xiao, K Wu, X Liang, R Li, KP Lai - Frontiers in Immunology, 2021 - frontiersin.org
Myasthenia gravis (MG) is an autoimmune disease primarily mediated by acetylcholine
receptor antibodies (AChR-Ab), cellular immune dependence, and complement system …

Monoclonal antibodies capable of inhibiting complement downstream of C5 in multiple species

WM Zelek, BP Morgan - Frontiers in Immunology, 2020 - frontiersin.org
Better understanding of roles of complement in pathology has fuelled an explosion of
interest in complement-targeted therapeutics. The C5-blocking monoclonal antibody (mAb) …

Second-generation C5 inhibitors for paroxysmal nocturnal hemoglobinuria

B Fattizzo, AG Kulasekararaj - BioDrugs, 2020 - Springer
The C5 targeting monoclonal antibody eculizumab has changed the natural history of
paroxysmal nocturnal hemoglobinuria (PNH) in the last 10 years. However, some unmet …

TMT-based quantitative proteomic analysis of cumulus cells derived from vitrified porcine immature oocytes following in vitro maturation

BY Jia, DC Xiang, SN Liu, B Zhang, QY Shao… - Theriogenology, 2020 - Elsevier
As the immature oocytes are submitted to cryopreservation, their surrounding cumulus cells
(CCs) will inevitably suffer, which may have some adverse effects on subsequent oocyte …

[HTML][HTML] Targeting terminal pathway reduces brain complement activation, amyloid load and synapse loss, and improves cognition in a mouse model of dementia

WM Zelek, RJ Bevan, BP Morgan - Brain, Behavior, and Immunity, 2024 - Elsevier
Complement is dysregulated in the brain in Alzheimer's Disease and in mouse models of
Alzheimer's disease. Each of the complement derived effectors, opsonins, anaphylatoxins …

Characterizing the original anti‐C5 function‐blocking antibody, BB5. 1, for species specificity, mode of action and interactions with C5

WM Zelek, GE Menzies, A Brancale, B Stockinger… - …, 2020 - Wiley Online Library
The implication of complement in multiple diseases over the last 20 years has fuelled
interest in developing anti‐complement drugs. To date, the focus has been on C5; blocking …