The future of cystic fibrosis care: a global perspective

SC Bell, MA Mall, H Gutierrez, M Macek… - The Lancet …, 2020 - thelancet.com
Executive summary The past six decades have seen remarkable improvements in health
outcomes for people with cystic fibrosis, which was once a fatal disease of infants and young …

[HTML][HTML] ECFS best practice guidelines: the 2018 revision

C Castellani, AJA Duff, SC Bell, HGM Heijerman… - Journal of cystic …, 2018 - Elsevier
Developments in managing CF continue to drive dramatic improvements in survival. As
newborn screening rolls-out across Europe, CF centres are increasingly caring for cohorts of …

Cystic fibrosis lung disease: an overview

NL Turcios - Respiratory care, 2020 - rc.rcjournal.com
Although better insights into the natural course of cystic fibrosis (CF) have led to treatment
approaches that have improved pulmonary health and increased the life expectancy of …

[HTML][HTML] Cystic Fibrosis Foundation consensus guidelines for the care of individuals with advanced cystic fibrosis lung disease

SG Kapnadak, E Dimango, D Hadjiliadis… - Journal of Cystic …, 2020 - Elsevier
Background Advanced cystic fibrosis lung disease (ACFLD) is common, is associated with
reduced quality of life, and remains the most frequent cause of death in individuals with …

[HTML][HTML] Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines

KJ Ramos, PJ Smith, EF McKone, JM Pilewski… - Journal of Cystic …, 2019 - Elsevier
Objective Provide recommendations to the cystic fibrosis (CF) community to facilitate timely
referral for lung transplantation for individuals with CF. Methods The CF Foundation …

Survival comparison of patients with cystic fibrosis in Canada and the United States: a population-based cohort study

AL Stephenson, J Sykes, S Stanojevic… - Annals of internal …, 2017 - acpjournals.org
Background: In 2011, the median age of survival of patients with cystic fibrosis reported in
the United States was 36.8 years, compared with 48.5 years in Canada. Direct comparison …

Burkholderia cenocepacia Infections in Cystic Fibrosis Patients: Drug Resistance and Therapeutic Approaches

VC Scoffone, LR Chiarelli, G Trespidi… - Frontiers in …, 2017 - frontiersin.org
Burkholderia cenocepacia is an opportunistic pathogen particularly dangerous for cystic
fibrosis (CF) patients. It can cause a severe decline in CF lung function possibly developing …

[PDF][PDF] Socioeconomic status and its relationship to chronic respiratory disease

S Sahni, A Talwar, S Khanijo… - Advances in respiratory …, 2017 - journals.viamedica.pl
Socioeconomic status (SES) is defined as an individual's social or economic standing, and
is a measure of an individual's or family's social or economic position or rank in a social …

Cystic fibrosis: emerging understanding and therapies

MM Rey, MP Bonk, D Hadjiliadis - Annual review of medicine, 2019 - annualreviews.org
Cystic fibrosis (CF) is the most common life-limiting genetic disease in Caucasian patients.
Continued advances have led to improved survival, and adults with CF now outnumber …

Socioeconomic status and health outcomes: cystic fibrosis as a model

GR Oates, MS Schechter - Expert review of respiratory medicine, 2016 - Taylor & Francis
ABSTRACT Introduction: Socioeconomic status (SES), which indicates one's access to
financial, educational, and social resources, is a powerful determinant of health outcomes in …