Congenital lung malformations

F Pederiva, SS Rothenberg, N Hall… - Nature Reviews …, 2023 - nature.com
Congenital lung malformations (CLMs) are rare developmental anomalies of the lung,
including congenital pulmonary airway malformations (CPAM), bronchopulmonary …

Congenital lung malformations: dysregulated lung developmental processes and altered signaling pathways

F Doktor, L Antounians, M Lacher, A Zani - Seminars in Pediatric Surgery, 2022 - Elsevier
Congenital lung malformations comprise a diverse group of anomalies including congenital
pulmonary airway malformation (CPAM, previously known as congenital cystic adenomatoid …

Pleuropulmonary blastoma in pediatric lung lesions

SM Kunisaki, DR Lal, JM Saito, ME Fallat… - …, 2021 - publications.aap.org
BACKGROUND: Pediatric lung lesions are a group of mostly benign pulmonary anomalies
with a broad spectrum of clinical disease and histopathology. Our objective was to evaluate …

Genomic instability in congenital lung malformations in children

R Rodrigues de Moura, S Patrizi, E Athanasakis… - Pediatric Surgery …, 2024 - Springer
Purpose To study the biological relationship between congenital lung malformations (CLMs)
and malignancy. Methods Biopsies of 12 CPAMs, 6 intralobar sequestrations and 2 …

Application of second-generation sequencing in congenital pulmonary airway malformations

G Zhang, C Cai, X Li, L Lou, B Zhou, H Zeng, X Yan… - Scientific Reports, 2022 - nature.com
To investigate the differential expression of genes in whole transcripts of congenital
pulmonary airway malformation (CPAM) using second-generation sequencing (also known …

Congenital pulmonary airway malformation: A case report of a rare cause of neonatal respiratory distress and review of the literature

EA Disu, OA Kehinde, AL Anga… - Nigerian Journal of …, 2019 - journals.lww.com
Congenital pulmonary airway malformation (CPAM), formerly known as congenital cystic
adenomatoid malformation (CCAM), is a rare developmental dysplastic lesion of the fetal …

In vitro models of fetal lung development to enhance research into congenital lung diseases

S Shibuya, J Allen-Hyttinen, P De Coppi… - Pediatric Surgery …, 2021 - Springer
Purpose This paper aims to build upon previous work to definitively establish in vitro models
of murine pseudoglandular stage lung development. These can be easily translated to …

[HTML][HTML] Congenital pulmonary airway malformation (CPAM): A case report and review of the literature

K Aryal, PR Regmi, G Adhikari, U Bhhattarai… - Radiology Case …, 2023 - Elsevier
Congenital pulmonary airway malformation (CPAM) is a rare congenital dysplastic
malformation characterized by failure of bronchial development and localized glandular …

Major surgical conditions of childhood and their lifelong implications: comprehensive review

PS Cullis, D Fouad, AM Goldstein, KKY Wong… - BJS open, 2024 - academic.oup.com
Background In recent decades, the survival of children with congenital anomalies and
paediatric cancer has improved dramatically such that there has been a steady shift towards …

EpCAM+CD73+ mark epithelial progenitor cells in postnatal human lung and are associated with pathogenesis of pulmonary disease including lung …

L Wang, P Dorn, C Simillion… - … of Physiology-Lung …, 2020 - journals.physiology.org
Lung injury in mice induces mobilization of discrete subsets of epithelial progenitor cells to
promote new airway and alveolar structures. However, whether similar cell types exist in …