Cardiac involvement in systemic sclerosis: getting to the heart of the matter

C Bruni, L Ross - Best Practice & Research Clinical Rheumatology, 2021 - Elsevier
Primary systemic sclerosis heart involvement (pSHI) is an important disease manifestation
that accounts for a significant proportion of systemic sclerosis (SSc)-associated mortality. A …

Screening for pulmonary arterial hypertension in systemic sclerosis

J Weatherald, D Montani, M Jevnikar… - European …, 2019 - Eur Respiratory Soc
Pulmonary arterial hypertension (PAH) is a dreaded complication of systemic sclerosis (SSc)
that occurs in∼ 10% of patients. Most individuals present with severe symptoms, significant …

Recommendations for screening and detection of connective tissue disease–associated pulmonary arterial hypertension

D Khanna, H Gladue, R Channick… - Arthritis & …, 2013 - Wiley Online Library
Objective Pulmonary arterial hypertension (PAH) affects up to 15% of patients with
connective tissue diseases (CTDs). Previous recommendations developed as part of larger …

Connective tissue disease-associated pulmonary arterial hypertension in Chinese patients

YJ Hao, X Jiang, W Zhou, Y Wang… - European …, 2014 - Eur Respiratory Soc
We sought to investigate the characteristics, survival and risk factors for mortality in Chinese
patients with connective tissue disease (CTD)-associated pulmonary arterial hypertension …

[HTML][HTML] Unique predictors of mortality in patients with pulmonary arterial hypertension associated with systemic sclerosis in the REVEAL registry

L Chung, HW Farber, R Benza, DP Miller, L Parsons… - Chest, 2014 - Elsevier
BACKGROUND: Patients with pulmonary arterial hypertension (PAH) associated with
systemic sclerosis (SSc-APAH) experience higher mortality rates than patients with …

Prevalence and risk factors for pulmonary arterial hypertension in patients with lupus

A Prabu, K Patel, CS Yee, P Nightingale… - …, 2009 - academic.oup.com
Objectives. Pulmonary arterial hypertension (PAH) is associated with rapid deterioration and
poor prognosis in SLE, especially during pregnancy. The prevalence of PAH in SLE in non …

Improved survival for patients with systemic sclerosis–associated pulmonary arterial hypertension: the Johns Hopkins Registry

HJ Hassan, M Naranjo, N Ayoub, T Housten… - American journal of …, 2023 - atsjournals.org
Rationale: To date, it remains unclear whether recent changes in the management of
patients with systemic sclerosis–associated pulmonary hypertension (SSc-PH) have …

Pulmonary arterial hypertension associated with connective tissue diseases (CTD-PAH): Recent and advanced data

B Thoreau, L Mouthon - Autoimmunity Reviews, 2023 - Elsevier
Pulmonary arterial hypertension (PAH), corresponding to group 1 of pulmonary
hypertension classification, is a rare disease with a major prognostic impact on morbidity …

Pulmonary hypertension in connective tissue diseases: epidemiology, pathogenesis, and treatment

DÜ Cansu, C Korkmaz - Clinical Rheumatology, 2023 - Springer
Pulmonary hypertension (PH) is a clinical condition characterized by increased pulmonary
arterial pressure arising from a heterogeneous range of diseases that has a deteriorating …

Lung involvements in rheumatic diseases: update on the epidemiology, pathogenesis, clinical features, and treatment

YJ Ha, YJ Lee, EH Kang - BioMed research international, 2018 - Wiley Online Library
Lung illness encountered in patients with rheumatic diseases bears clinical significance in
terms of increased morbidity and mortality as well as potential challenges placed on patient …