Systemic sclerosis-associated interstitial lung disease
A Perelas, RM Silver, AV Arrossi… - The Lancet respiratory …, 2020 - thelancet.com
Systemic sclerosis is an autoimmune connective tissue disease, which is characterised by
immune dysregulation and progressive fibrosis that typically affects the skin, with variable …
immune dysregulation and progressive fibrosis that typically affects the skin, with variable …
Presentation, diagnosis and clinical course of the spectrum of progressive-fibrosing interstitial lung diseases
V Cottin, NA Hirani, DL Hotchkin… - European …, 2018 - Eur Respiratory Soc
Although these conditions are rare, a proportion of patients with interstitial lung diseases
(ILDs) may develop a progressive-fibrosing phenotype. Progressive fibrosis is associated …
(ILDs) may develop a progressive-fibrosing phenotype. Progressive fibrosis is associated …
Interstitial lung disease associated with systemic sclerosis (SSc-ILD)
V Cottin, KK Brown - Respiratory research, 2019 - Springer
Abstract Background Systemic sclerosis (SSc) is a rare connective tissue disease with a
heterogeneous clinical course. Interstitial lung disease (ILD) is a common manifestation of …
heterogeneous clinical course. Interstitial lung disease (ILD) is a common manifestation of …
Predictors of progression in systemic sclerosis patients with interstitial lung disease
Systemic sclerosis (SSc) is a systemic autoimmune disease affecting multiple organ
systems, including the lungs. Interstitial lung disease (ILD) is the leading cause of death in …
systems, including the lungs. Interstitial lung disease (ILD) is the leading cause of death in …
Comorbidities in idiopathic pulmonary fibrosis patients: a systematic literature review
G Raghu, VC Amatto, J Behr… - European Respiratory …, 2015 - Eur Respiratory Soc
Idiopathic pulmonary fibrosis (IPF) is associated with a fatal prognosis and manifests in
patients over 60 years old who may have comorbidities. The prevalence and impact of …
patients over 60 years old who may have comorbidities. The prevalence and impact of …
Short‐term pulmonary function trends are predictive of mortality in interstitial lung disease associated with systemic sclerosis
NS Goh, RK Hoyles, CP Denton… - Arthritis & …, 2017 - Wiley Online Library
Objective To determine the prognostic value of pulmonary function test (PFT) trends at 1 and
2 years in interstitial lung disease (ILD) associated with systemic sclerosis (SSc). Methods …
2 years in interstitial lung disease (ILD) associated with systemic sclerosis (SSc). Methods …
Pulmonary manifestations of Sjögren's syndrome
T Flament, A Bigot, B Chaigne… - European …, 2016 - Eur Respiratory Soc
In 9–20% of cases, Sjögren's syndrome is associated with various respiratory symptoms.
The most typical manifestations are chronic interstitial lung disease (ILD) and …
The most typical manifestations are chronic interstitial lung disease (ILD) and …
Interstitial lung disease in systemic sclerosis: a simple staging system
NSL Goh, SR Desai, S Veeraraghavan… - American journal of …, 2008 - atsjournals.org
Rationale: In interstitial lung disease complicating systemic sclerosis (SSc-ILD), the optimal
prognostic use of baseline pulmonary function tests (PFTs) and high-resolution computed …
prognostic use of baseline pulmonary function tests (PFTs) and high-resolution computed …
A multicenter, prospective, randomized, double‐blind, placebo‐controlled trial of corticosteroids and intravenous cyclophosphamide followed by oral azathioprine for …
RK Hoyles, RW Ellis, J Wellsbury… - … : Official Journal of …, 2006 - Wiley Online Library
Objective The lack of randomized controlled trials (RCTs) in pulmonary fibrosis in systemic
sclerosis (SSc) has hampered an evidence‐based approach to treatment. This RCT was …
sclerosis (SSc) has hampered an evidence‐based approach to treatment. This RCT was …
Scleroderma lung disease
JJ Solomon, AL Olson, A Fischer, T Bull… - European respiratory …, 2013 - Eur Respiratory Soc
Systemic sclerosis (SSc) is a systemic autoimmune disease that is characterised by
endothelial dysfunction resulting in a small-vessel vasculopathy, fibroblast dysfunction with …
endothelial dysfunction resulting in a small-vessel vasculopathy, fibroblast dysfunction with …