TP53 in bone and soft tissue sarcomas

E Thoenen, A Curl, T Iwakuma - Pharmacology & therapeutics, 2019 - Elsevier
Genomic and functional study of existing and emerging sarcoma targets, such as fusion
proteins, chromosomal aberrations, reduced tumor suppressor activity, and oncogenic …

Therapeutic advances in leiomyosarcoma

K Lacuna, S Bose, M Ingham, G Schwartz - Frontiers in Oncology, 2023 - frontiersin.org
Leiomyosarcoma is an aggressive mesenchymal malignancy and represents one of the
most common subtypes of soft tissue sarcomas. It is characterized by significant disease …

Pan-Cancer Analysis of BRCA1 and BRCA2 Genomic Alterations and Their Association With Genomic Instability as Measured by Genome-Wide Loss of …

ES Sokol, D Pavlick, H Khiabanian… - JCO precision …, 2020 - ascopubs.org
PURPOSE BRCA1 or BRCA2 loss of function results in homologous recombination
deficiency (HRD), which is targetable by poly (ADP-ribose) polymerase (PARP) inhibitors …

Phase II study of olaparib and temozolomide for advanced uterine leiomyosarcoma (NCI Protocol 10250)

M Ingham, JB Allred, L Chen, B Das… - Journal of Clinical …, 2023 - ascopubs.org
PURPOSE Uterine leiomyosarcoma (uLMS) is an aggressive subtype of soft-tissue sarcoma
with frequent metastatic relapse after curative surgery. Chemotherapy provides limited …

Genomic database analysis of uterine leiomyosarcoma mutational profile

A Astolfi, M Nannini, V Indio, A Schipani, A Rizzo… - Cancers, 2020 - mdpi.com
Uterine Leiomyosarcoma (uLMS) is by far the most common type of uterine sarcoma,
characterized by an aggressive clinical course, a heterogeneous genetic profile and a very …

Comprehensive review of uterine leiomyosarcoma: pathogenesis, diagnosis, prognosis, and targeted therapy

Q Yang, OS Madueke-Laveaux, H Cun, M Wlodarczyk… - Cells, 2024 - mdpi.com
Uterine leiomyosarcoma (uLMS) is the most common subtype of uterine sarcomas. They
have a poor prognosis with high rates of recurrence and metastasis. The five-year survival …

Clinical utility of CDK4/6 inhibitors in sarcoma: successes and future challenges

JY Hsu, ND Seligson, JL Hays, WO Miles… - JCO Precision …, 2022 - ascopubs.org
PURPOSE Soft tissue and bone sarcomas are rare malignancies that exhibit significant
pathologic and molecular heterogeneity. Deregulation of the CDKN2A-CCND-CDK4/6 …

Hyper-Dependence on NHEJ Enables Synergy between DNA-PK Inhibitors and Low-Dose Doxorubicin in Leiomyosarcoma

A Marino-Enriquez, JP Novotny, DC Gulhan… - Clinical Cancer …, 2023 - AACR
Purpose: Leiomyosarcoma (LMS) is an aggressive sarcoma for which standard
chemotherapies achieve response rates under 30%. There are no effective targeted …

Targeting homologous recombination deficiency in uterine leiomyosarcoma

G Dall, CJ Vandenberg, K Nesic, G Ratnayake… - Journal of Experimental …, 2023 - Springer
Background Uterine leiomyosarcoma (uLMS) is a rare and aggressive gynaecological
malignancy, with individuals with advanced uLMS having a five-year survival of< 10 …

Homologous recombination repair deficiency as a therapeutic target in sarcoma

J Oza, SD Doshi, L Hao, E Musi, GK Schwartz… - Seminars in …, 2020 - Elsevier
Sarcoma is a rare cancer arising from soft tissue and bone and consists of more than 50
distinct subtypes. There is an increasing emphasis on understanding the cancer biology of …