STEC-HUS, atypical HUS and TTP are all diseases of complement activation
Haemolytic uraemic syndrome (HUS) and thrombotic thrombocytopaenic purpura (TTP) are
diseases characterized by microvascular thrombosis, with consequent thrombocytopaenia …
diseases characterized by microvascular thrombosis, with consequent thrombocytopaenia …
Characterization and treatment of congenital thrombotic thrombocytopenic purpura
F Alwan, C Vendramin, R Liesner… - Blood, The Journal …, 2019 - ashpublications.org
Congenital thrombotic thrombocytopenic purpura (cTTP) is an ultra-rare
thrombomicroangiopathy caused by an inherited deficiency of a disintegrin and …
thrombomicroangiopathy caused by an inherited deficiency of a disintegrin and …
Pathophysiology of thrombotic thrombocytopenic purpura
HM Tsai - International journal of hematology, 2010 - Springer
Thrombotic thrombocytopenic purpura (TTP) is a disorder with characteristic von Willebrand
factor (VWF)-rich microthrombi affecting the arterioles and capillaries of multiple organs. The …
factor (VWF)-rich microthrombi affecting the arterioles and capillaries of multiple organs. The …
Natural history of Upshaw–Schulman syndrome based on ADAMTS13 gene analysis in Japan
Y Fujimura, M Matsumoto, A Isonishi… - … of Thrombosis and …, 2011 - Wiley Online Library
Upshaw–Schulman syndrome (USS) is an extremely rare hereditary deficiency of
ADAMTS13 activity, termed congenital TTP. The clinical signs are usually mild during …
ADAMTS13 activity, termed congenital TTP. The clinical signs are usually mild during …
An update on pathogenesis and diagnosis of thrombotic thrombocytopenic purpura
BS Joly, P Coppo, A Veyradier - Expert review of hematology, 2019 - Taylor & Francis
Introduction: Thrombotic thrombocytopenic purpura (TTP) is a rare and life-threatening
thrombotic microangiopathy characterized by microangiopathic hemolytic anemia …
thrombotic microangiopathy characterized by microangiopathic hemolytic anemia …
ADAMTS13 mutations and polymorphisms in congenital thrombotic thrombocytopenic purpura
LA Lotta, I Garagiola, R Palla, A Cairo… - Human …, 2010 - Wiley Online Library
Congenital thrombotic thrombocytopenic purpura (TTP)(also known as Upshaw‐Schulman
syndrome, USS) is a rare, life‐threatening disease characterized by thrombocytopenia and …
syndrome, USS) is a rare, life‐threatening disease characterized by thrombocytopenia and …
Residual plasmatic activity of ADAMTS13 is correlated with phenotype severity in congenital thrombotic thrombocytopenic purpura
LA Lotta, HM Wu, IJ Mackie, M Noris… - Blood, The Journal …, 2012 - ashpublications.org
The quantification of residual plasmatic ADAMTS13 activity in congenital thrombotic
thrombocytopenic purpura (TTP) patients is constrained by limitations in sensitivity and …
thrombocytopenic purpura (TTP) patients is constrained by limitations in sensitivity and …
Pediatric thrombotic thrombocytopenic purpura
BS Joly, P Coppo, A Veyradier - European journal of …, 2018 - Wiley Online Library
Child‐onset thrombotic thrombocytopenic purpura (TTP) is a rare entity of thrombotic
microangiopathy (TMA). The pathophysiology of the disease is based on a severe functional …
microangiopathy (TMA). The pathophysiology of the disease is based on a severe functional …
Thrombotic thrombocytopenic purpura: a thrombotic disorder caused by ADAMTS13 deficiency
HM Tsai - Hematology/oncology clinics of North America, 2007 - Elsevier
A serious disorder with characteristic microvascular thrombosis involving the brain and other
organs, thrombotic thrombocytopenic purpura (TTP) typically presents with …
organs, thrombotic thrombocytopenic purpura (TTP) typically presents with …
ADAMTS13 gene mutations influence ADAMTS13 conformation and disease age-onset in the French Cohort of Upshaw–Schulman syndrome
BS Joly, P Boisseau, E Roose… - Thrombosis and …, 2018 - thieme-connect.com
Background Congenital thrombotic thrombocytopaenic purpura (TTP) or Upshaw–Schulman
syndrome (USS) is a rare, life-threatening, inherited thrombotic microangiopathy (TMA). USS …
syndrome (USS) is a rare, life-threatening, inherited thrombotic microangiopathy (TMA). USS …