Idiopathic pulmonary fibrosis (IPF), also termed cryptogenic fibrosing alveolitis, is a
clinicopathological syndrome characterised by cough, exertional dyspneoa, basilar crackles …

Interstitial lung disease (ILD) is a challenging clinical entity associated with multiple
connective tissue diseases, and is a significant cause of morbidity and mortality. Effective …

This document is an international evidence-based guideline on the diagnosis and
management of idiopathic pulmonary fibrosis, and is a collaborative effort of the American …

Rationale: Mortality rates from rheumatoid arthritis–associated interstitial lung disease (RA-
ILD) are largely unknown. Objectives: We sought to determine mortality rates from …

Rationale: The clinical management of idiopathic pulmonary fibrosis (IPF) remains a major
challenge due to lack of effective drug therapy or accurate indicators for disease …

Rationale: From the late 1970s to the early 1990s, studies found that mortality rates for
pulmonary fibrosis were increasing. Recent data for mortality from pulmonary fibrosis are …

Usual interstitial pneumonia (UIP) is a specific histopathologic pattern of interstitial lung
fibrosis that may be idiopathic or secondary to autoimmune diseases and environmental …

Background Bone marrow-derived fibrocytes reportedly play important roles in the
pathogenesis of idiopathic pulmonary fibrosis. Pirfenidone is an anti-fibrotic agent; however …

OVERVIEW OF IPF AND EVIDENCE-BASED GUIDELINES of patients with a radiographic
and histopathologic pattern of usual interstitial pneumonia (UIP) and no other identifiable …

Pulmonary fibrosis is a pathological condition in which lungs become scarred due to the
excess extracellular matrix (ECM) deposition and structural alterations in the interstitium of …