This is a unique state of the art review written by a group of 21 international recognized
experts in the field that gathered during a meeting organized by the European …

This review article describes definitive noninvasive respiratory management of respiratory
muscle dysfunction to eliminate need to resort to tracheotomy. In 2010 clinicians from 22 …

INTRODUCTION Clinical context and need for a guideline Neuromuscular diseases as a
group are relatively common with a prevalence of about 1 in 3000. The majority of these …

Background Respiratory failure is a significant concern in neuromuscular diseases (NMDs).
This CHEST guideline examines the literature on the respiratory management of patients …

Objective Respiratory management of patients with end-stage respiratory muscle failure of
neuromuscular disease has evolved from no treatment and inevitable respiratory failure to …

The European Neuromuscular Centre (ENMC) convened the 228th ENMC Workshop on
airway clearance techniques (ACT) in neuromuscular disorders (NMD) in Naarden, The …

McKim DA, Katz SL, Barrowman N, Ni A, LeBlanc C. Lung volume recruitment slows
pulmonary function decline in Duchenne muscular dystrophy. OBJECTIVE: To evaluate the …

Background: Mechanical insufflation-exsufflation (MI-E), more commonly known as 'cough
assist therapy', is a method which produces inspiratory and expiratory assistance to improve …

Respiratory muscle weakness is a major cause of morbidity and mortality in patients with
neuromuscular diseases (NMDs). Respiratory involvement in NMDs can manifest broadly …

Over the last 30 to 40 years, improvements in technology, as well as changing clinical
practice regarding the appropriateness of long-term ventilation in patients with “non-curable” …