Amyotrophic lateral sclerosis is characterised by the progressive loss of motor neurons in
the brain and spinal cord. This neurodegenerative syndrome shares pathobiological …

This article presents the revised consensus criteria for the diagnosis of frontotemporal
dysfunction in amyotrophic lateral sclerosis (ALS) based on an international research …

Early reports of cognitive and behavioural deficits in motor neuron disease might have been
overlooked initially, but the concept of a frontotemporal dementia-motor neuron disease …

Background: The evidence base for the diagnosis and management of amyotrophic lateral
sclerosis (ALS) is weak. Objectives: To provide evidence‐based or expert recommendations …

This study presents the Edinburgh Cognitive and Behavioural ALS Screen (ECAS),
developed for ALS patients with physical disability for use by health care professionals. The …

Amyotrophic lateral sclerosis (ALS) is a neurodegenerative disease that results in
progressive loss of bulbar and limb function. Patients typically die from respiratory failure …

Increased awareness of cognitive and behavioural change in amyotrophic lateral sclerosis
has been driven by various clinic-based and population-based studies. A frontotemporal …

Significant progress has been made in understanding the pre-symptomatic phase of
amyotrophic lateral sclerosis. While much is still unknown, advances in other …

Numerous kindreds with familial frontotemporal dementia and/or amyotrophic lateral
sclerosis have been linked to chromosome 9, and an expansion of the GGGGCC …

The non-fluent/agrammatic variant of primary progressive aphasia (naPPA) is a young-onset
neurodegenerative disorder characterised by poor grammatical comprehension and …