Vascular Behçet syndrome: from pathogenesis to treatment

A Bettiol, F Alibaz-Oner, H Direskeneli… - Nature Reviews …, 2023 - nature.com
Behçet syndrome is a rare, chronic inflammatory disease of unknown aetiopathogenesis,
most commonly presenting with mucocutaneous and ocular manifestations. Vascular …

Neuro-Behcet's disease: an update on diagnosis, differential diagnoses, and treatment

A Borhani-Haghighi, B Kardeh, S Banerjee… - Multiple sclerosis and …, 2020 - Elsevier
Neuro-Behcet's disease (NBD) is defined as a combination of neurologic symptoms and/or
signs in a patient with Behcet's disease (BD). Relevant syndromes include brainstem …

Behçet's disease: How to diagnose and treat vascular involvement

E Seyahi - Best practice & research Clinical rheumatology, 2016 - Elsevier
Behçet's disease is a multisystem disorder with unknown etiology and a unique geographic
distribution. The disease is characterized by recurrent skin–mucosa lesions and sight …

A20 haploinsufficiency (HA20): clinical phenotypes and disease course of patients with a newly recognised NF-kB-mediated autoinflammatory disease

FA Aeschlimann, ED Batu, SW Canna, E Go… - Annals of the …, 2018 - ard.bmj.com
Objectives The association between mutations in TNFAIP3, encoding the NF-kB regulatory
protein A20, and a new autoinflammatory disease has recently been recognised. This study …

French recommendations for the management of Behçet's disease

I Kone-Paut, S Barete, B Bodaghi, K Deiva… - Orphanet journal of rare …, 2021 - Springer
Behçet's disease (BD) is a systemic variable vessel vasculitis that involves the skin, mucosa,
joints, eyes, arteries, veins, nervous system and gastrointestinal system, presenting with …

Pediatric Behçet's disease

M Yildiz, F Haslak, A Adrovic, S Sahin, O Koker… - Frontiers in …, 2021 - frontiersin.org
Behçet's Disease (BD) is a systemic vasculitis firstly described as a disorder causing
aphthous lesion in oral and genital mucosae and uveitis. The disease has an extremely …

Neuro-Behçet syndrome

S Saip, G Akman-Demir, A Siva - Handbook of clinical neurology, 2014 - Elsevier
Behçet syndrome (BS) is an idiopathic chronic relapsing multisystem vascular-inflammatory
disease of unknown origin. As the disease affects many organs and systems and shows a …

Behçet's Syndrome and the Nervous System Involvement

U Uygunoglu, A Siva - Neuroimmune Diseases: From Cells to the Living …, 2024 - Springer
Behcet's syndrome (BS) is a chronic, recurrent relapsing multisystem vascular-inflammatory
syndrome of unknown etiology that predominantly affects veins. Although BS was initially …

Vasculitis in systemic autoinflammatory diseases

S Demir, E Sag, F Dedeoglu, S Ozen - Frontiers in Pediatrics, 2018 - frontiersin.org
Autoinflammatory diseases (AID) are diseases of the innate immune system, characterized
by recurrent episodes of localized or systemic inflammation. Vasculitis may accompany AID …

Behçet's syndrome: providing integrated care

SN Esatoglu, Z Kutlubay, D Ucar, I Hatemi… - Journal of …, 2017 - Taylor & Francis
Behçet's syndrome (BS) is a multisystem vasculitis that presents with a variety of
mucocutaneous manifestations such as oral and genital ulcers, papulopustular lesions and …