Calcium signaling and cardiac arrhythmias

AP Landstrom, D Dobrev, XHT Wehrens - Circulation research, 2017 - Am Heart Assoc
There has been a significant progress in our understanding of the molecular mechanisms by
which calcium (Ca2+) ions mediate various types of cardiac arrhythmias. A growing list of …

Mechanisms of Altered Ca2+ Handling in Heart Failure

M Luo, ME Anderson - Circulation research, 2013 - Am Heart Assoc
Ca2+ plays a crucial role in connecting membrane excitability with contraction in
myocardium. The hallmark features of heart failure are mechanical dysfunction and …

Cardiac T-tubule microanatomy and function

TT Hong, RM Shaw - Physiological reviews, 2017 - journals.physiology.org
Unique to striated muscle cells, transverse tubules (t-tubules) are membrane organelles that
consist of sarcolemma penetrating into the myocyte interior, forming a highly branched and …

The physiology and pathophysiology of T-tubules in the heart

IE Setterberg, C Le, M Frisk, H Perdreau-Dahl… - Frontiers in …, 2021 - frontiersin.org
In cardiomyocytes, invaginations of the sarcolemmal membrane called t-tubules are critically
important for triggering contraction by excitation-contraction (EC) coupling. These structures …

The role of junctophilin proteins in cellular function

SE Lehnart, XHT Wehrens - Physiological reviews, 2022 - journals.physiology.org
Junctophilins (JPHs) comprise a family of structural proteins that connect the plasma
membrane to intracellular organelles such as the endo/sarcoplasmic reticulum (ER/SR) …

Mutation E169K in junctophilin-2 causes atrial fibrillation due to impaired RyR2 stabilization

DL Beavers, W Wang, S Ather, N Voigt… - Journal of the American …, 2013 - jacc.org
Objectives: This study sought to study the role of junctophilin-2 (JPH2) in atrial fibrillation
(AF). Background: JPH2 is believed to have an important role in sarcoplasmic reticulum (SR) …

Emerging mechanisms of T-tubule remodelling in heart failure

A Guo, C Zhang, S Wei, B Chen… - Cardiovascular …, 2013 - academic.oup.com
Cardiac excitation–contraction coupling occurs primarily at the sites of transverse (T)-
tubule/sarcoplasmic reticulum junctions. The orderly T-tubule network guarantees the …

Stimulated emission depletion live-cell super-resolution imaging shows proliferative remodeling of T-tubule membrane structures after myocardial infarction

E Wagner, MA Lauterbach, T Kohl, V Westphal… - Circulation …, 2012 - Am Heart Assoc
Rationale: Transverse tubules (TTs) couple electric surface signals to remote intracellular
Ca2+ release units (CRUs). Diffraction-limited imaging studies have proposed loss of TT …

Interaction of the Joining Region in Junctophilin-2 With the L-Type Ca2+ Channel Is Pivotal for Cardiac Dyad Assembly and Intracellular Ca2+ Dynamics

P Gross, J Johnson, CM Romero, DM Eaton… - Circulation …, 2021 - Am Heart Assoc
Rationale: Ca2+-induced Ca2+ release (CICR) in normal hearts requires close
approximation of L-type calcium channels (LTCCs) within the transverse tubules (T-tubules) …

EC coupling structural protein junctophilin-2 encodes a stress-adaptive transcription regulator

A Guo, Y Wang, B Chen, Y Wang, J Yuan, L Zhang… - Science, 2018 - science.org
INTRODUCTION Cardiac excitation-contraction (EC) coupling refers to a cascade of Ca2+-
mediated events whereby membrane depolarization leads to cell contraction. At the …