Familial Mediterranean fever, from pathogenesis to treatment: a contemporary review

A Tufan, H LACHMANN - Turkish Journal of Medical …, 2020 - journals.tubitak.gov.tr
Abstract Familial Mediterranean fever (FMF)(OMIM# 249100) is the most common hereditary
autoinflammatory disease in the world. FMF is caused by gain of function mutations of MEFV …

Amyloidosis and glomerular diseases in familial Mediterranean fever

R Siligato, G Gembillo, V Calabrese, G Conti… - Medicina, 2021 - mdpi.com
Familial Mediterranean fever (FMF) is a genetic autoinflammatory disease with autosomal
recessive transmission, characterized by periodic fever attacks with self-limited serositis …

Predictors of persistent inflammation in familial Mediterranean fever and association with damage

H Babaoglu, B Armagan, E Bodakci, H Satis… - …, 2021 - academic.oup.com
Objective Persistent inflammation is an insidious and less studied feature of FMF. We
investigated clinical determinants of persistent inflammation and its associations with …

Behçet disease, familial Mediterranean fever and MEFV variations: More than just an association

E Seyahi, S Ugurlu, S Amikishiyev, A Gul - Clinical Immunology, 2023 - Elsevier
Behçet disease (BD) and familial Mediterranean fever (FMF) are two inflammatory disorders
that share many features including historical background, ethnical distribution and …

Bibliometric analysis of publication activity in the field of familial Mediterranean fever in 2010–2019: a Scopus-based study

BF Kocyigit, A Akyol - Rheumatology International, 2021 - Springer
Familial Mediterranean fever (FMF) is a systemic autoinflammatory disease, which presents
with recurrent episodes of fever, serositis, synovial inflammation and various different clinical …

Spondyloarthritis in familial Mediterranean fever: a cohort study

S Acer Kasman, MT Duruöz - Rheumatology International, 2022 - Springer
Familial Mediterranean fever (FMF) and spondyloarthritis (SpA) may show several common
signs. This study aimed to evaluate the frequency of SpA and its manifestations in FMF, the …

The preferential use of anakinra in various settings of FMF: a review applied to an updated treatment-related perspective of the disease

E Giat, I Ben-Zvi, M Lidar, A Livneh - International journal of molecular …, 2022 - mdpi.com
Familial Mediterranean fever (FMF), the most frequent monogenic autoinflammatory
disease, is manifested with recurrent and chronic inflammation and amyloid A (AA) …

Tripartite motif family proteins in inflammatory bowel disease: Mechanisms and potential for interventions

R Chen, Y Tie, J Lu, L Li, Z Zeng, M Chen… - Cell …, 2022 - Wiley Online Library
Inflammatory bowel disease (IBD) is a chronic recurrent gastrointestinal inflammatory
disease that poses a heavy burden to the global healthcare system. However, the current …

[PDF][PDF] Long-term safety and efficacy of anakinra and canakinumab in patients with familial Mediterranean fever: a single-centre real-life study with 101 patients

N Atas, GA Eroglu, HN Sodan, BO Ozturk… - Clin Exp …, 2021 - clinexprheumatol.org
Objective. Anakinra and canakinumab are the most commonly used agents in colchicine
resistant/intolerant patients. In this study we investigated long-term efficacy and safety of …

IgA vasculitis nephritis

E Nüsken, LT Weber - Current Opinion in Pediatrics, 2022 - journals.lww.com
Close surveillance of all IgAV patients for renal involvement is recommended. Given the
multilevel pathogenesis, early treatment of even mild cases should be initiated. Further …