Primary ciliary dyskinesia: an update on clinical aspects, genetics, diagnosis, and future treatment strategies
V Mirra, C Werner, F Santamaria - Frontiers in pediatrics, 2017 - frontiersin.org
Primary ciliary dyskinesia (PCD) is an orphan disease (MIM 244400), autosomal recessive
inherited, characterized by motile ciliary dysfunction. The estimated prevalence of PCD is 1 …
inherited, characterized by motile ciliary dysfunction. The estimated prevalence of PCD is 1 …
[HTML][HTML] European cystic fibrosis society standards of care: framework for the cystic fibrosis centre
S Conway, IM Balfour-Lynn, K De Rijcke… - Journal of Cystic …, 2014 - Elsevier
A significant increase in life expectancy in successive birth cohorts of people with cystic
fibrosis (CF) is a result of more effective treatment for the disease. It is also now widely …
fibrosis (CF) is a result of more effective treatment for the disease. It is also now widely …
Guidelines for the physiotherapy management of the adult, medical, spontaneously breathing patient
J Bott, S Blumenthal, M Buxton, S Ellum, C Falconer… - Thorax, 2009 - thorax.bmj.com
Conclusion This is the first extensive systematic literature review undertaken of the existing
evidence surrounding comprehensive physiotherapy management of the spontaneously …
evidence surrounding comprehensive physiotherapy management of the spontaneously …
Airway clearance techniques: the right choice for the right patient
S Belli, I Prince, G Savio, E Paracchini… - Frontiers in …, 2021 - frontiersin.org
The management of bronchial secretions is one of the main problems encountered in a wide
spectrum of medical conditions ranging from respiratory disorders, neuromuscular disorders …
spectrum of medical conditions ranging from respiratory disorders, neuromuscular disorders …
Cystic fibrosis pulmonary guidelines: airway clearance therapies
PA Flume, KA Robinson, BP O'Sullivan, JD Finder… - Respiratory …, 2009 - rc.rcjournal.com
Cystic fibrosis (CF) is a genetic disease characterized by dehydration of airway surface
liquid and impaired mucociliary clearance. As a result, there is difficulty clearing pathogens …
liquid and impaired mucociliary clearance. As a result, there is difficulty clearing pathogens …
Positive expiratory pressure physiotherapy for airway clearance in people with cystic fibrosis
M McIlwaine, B Button, SJ Nevitt - Cochrane Database of …, 2019 - cochranelibrary.com
Background Chest physiotherapy is widely prescribed to assist the clearance of airway
secretions in people with cystic fibrosis (CF). Positive expiratory pressure (PEP) devices …
secretions in people with cystic fibrosis (CF). Positive expiratory pressure (PEP) devices …
Physiotherapy for cystic fibrosis in Australia and New Zealand: a clinical practice guideline
BM Button, C Wilson, R Dentice, NS Cox… - …, 2016 - Wiley Online Library
Physiotherapy management is a key element of care for people with cystic fibrosis (CF)
throughout the lifespan. Although considerable evidence exists to support physiotherapy …
throughout the lifespan. Although considerable evidence exists to support physiotherapy …
Nonpharmacologic airway clearance therapies: ACCP evidence-based clinical practice guidelines
FD McCool, MJ Rosen - Chest, 2006 - Elsevier
Background: Airway clearance may be impaired in disorders associated with abnormal
cough mechanics, altered mucus rheology, altered mucociliary clearance, or structural …
cough mechanics, altered mucus rheology, altered mucociliary clearance, or structural …
Oscillating devices for airway clearance in people with cystic fibrosis
L Morrison, S Milroy - Cochrane database of systematic …, 2020 - cochranelibrary.com
Background Chest physiotherapy is widely prescribed to assist the clearance of airway
secretions in people with cystic fibrosis. Oscillating devices generate intra‐or extra‐thoracic …
secretions in people with cystic fibrosis. Oscillating devices generate intra‐or extra‐thoracic …
Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis
L Warnock, A Gates - Cochrane Database of Systematic …, 2015 - cochranelibrary.com
Background Chest physiotherapy is widely used in people with cystic fibrosis in order to
clear mucus from the airways. This is an updated version of previously published reviews …
clear mucus from the airways. This is an updated version of previously published reviews …