Idiopathic pulmonary fibrosis: state of the art for 2023

AJ Podolanczuk, CC Thomson… - European …, 2023 - Eur Respiratory Soc
Idiopathic pulmonary fibrosis (IPF) is a progressive fibrotic lung disease characterised by
worsening respiratory symptoms and physiological impairment. Increasing awareness of the …

A global view of pulmonary hypertension

MM Hoeper, M Humbert, R Souza, M Idrees… - The Lancet …, 2016 - thelancet.com
Pulmonary hypertension is a substantial global health issue. All age groups are affected with
rapidly growing importance in elderly people, particularly in countries with ageing …

Pulmonary fibrosis as a result of acute lung inflammation: molecular mechanisms, relevant in vivo models, prognostic and therapeutic approaches

IA Savin, MA Zenkova, AV Sen'kova - International journal of molecular …, 2022 - mdpi.com
Pulmonary fibrosis is a chronic progressive lung disease that steadily leads to lung
architecture disruption and respiratory failure. The development of pulmonary fibrosis is …

Riociguat for idiopathic interstitial pneumonia-associated pulmonary hypertension (RISE-IIP): a randomised, placebo-controlled phase 2b study

SD Nathan, J Behr, HR Collard, V Cottin… - The Lancet …, 2019 - thelancet.com
Background Idiopathic interstitial pneumonias are often complicated by pulmonary
hypertension, increasing morbidity and mortality. There are no approved treatments for …

[HTML][HTML] Nintedanib plus sildenafil in patients with idiopathic pulmonary fibrosis

M Kolb, G Raghu, AU Wells, J Behr… - … England Journal of …, 2018 - Mass Medical Soc
Background Nintedanib is an approved treatment for idiopathic pulmonary fibrosis (IPF). A
subgroup analysis of a previously published trial suggested that sildenafil may provide …

Treatment of idiopathic pulmonary fibrosis with ambrisentan: a parallel, randomized trial

G Raghu, J Behr, KK Brown, JJ Egan… - Annals of internal …, 2013 - acpjournals.org
Chinese translation This article has been corrected. The original version (PDF) is appended
to this article as a Supplement. Background: Idiopathic pulmonary fibrosis (IPF) is …

Impact of comorbidities on mortality in patients with idiopathic pulmonary fibrosis

M Kreuter, S Ehlers-Tenenbaum, K Palmowski… - PloS one, 2016 - journals.plos.org
Introduction Comorbidities significantly influence the clinical course of idiopathic pulmonary
fibrosis (IPF). However, their prognostic impact is not fully understood. We therefore aimed to …

Diastolic pulmonary vascular pressure gradient: a predictor of prognosis in “out-of-proportion” pulmonary hypertension

C Gerges, M Gerges, MB Lang, Y Zhang, J Jakowitsch… - Chest, 2013 - Elsevier
Background Left-sided heart disease (LHD) is the most common cause of pulmonary
hypertension (PH). In patients with LHD, elevated left atrial pressure causes a passive …

Pulmonary hypertension in patients with combined pulmonary fibrosis and emphysema syndrome

V Cottin, J Le Pavec, G Prévot, H Mal… - European respiratory …, 2010 - Eur Respiratory Soc
This study aims to describe the haemodynamic and survival characteristics of patients with
pulmonary hypertension in the recently individualised syndrome of combined pulmonary …

An official American Thoracic Society clinical practice guideline: diagnosis, risk stratification, and management of pulmonary hypertension of sickle cell disease

ES Klings, RF Machado, RJ Barst… - American journal of …, 2014 - atsjournals.org
Background: In adults with sickle cell disease (SCD), an increased tricuspid regurgitant
velocity (TRV) measured by Doppler echocardiography, an increased serum N-terminal pro …