Pulmonary arterial hypertension associated with connective tissue diseases (CTD-PAH): Recent and advanced data

B Thoreau, L Mouthon - Autoimmunity Reviews, 2023 - Elsevier
Pulmonary arterial hypertension (PAH), corresponding to group 1 of pulmonary
hypertension classification, is a rare disease with a major prognostic impact on morbidity …

Hematopoietic cell transplantation for systemic sclerosis—a review

D Levin, MS Osman, C Durand, H Kim, I Hemmati… - Cells, 2022 - mdpi.com
Systemic sclerosis (SSc) is an autoimmune, multi-organ, connective tissue disease
associated with significant morbidity and mortality. Conventional immunosuppressive …

Understanding and managing cardiac involvement in systemic sclerosis

GS Moysidou, A Dara, A Arvanitaki… - Expert Review of …, 2023 - Taylor & Francis
Introduction Cardiac involvement is common in systemic sclerosis occurring in up to 80% of
patients. Primary myocardial dysfunction results from impairment of coronary microvascular …

Contribution of left ventricular diastolic dysfunction to survival and breathlessness in systemic sclerosis–associated interstitial lung disease

JL Fairley, D Hansen, A Burns, D Prior… - The Journal of …, 2024 - jrheum.org
Objective To explore the effect of left ventricular (LV) diastolic dysfunction (LVDD) in
systemic sclerosis (SSc)-associated interstitial lung disease (ILD), and to investigate SSc …

Systemic Sclerosis Sine Scleroderma: A Time of Reappraisal

A Makris, A Panagiotopoulos, O Distler… - The Journal of …, 2024 - jrheum.org
Objective Systemic sclerosis sine scleroderma (ssSSc), formally described in 1962, is a
subset of SSc that, unlike limited cutaneous (lcSSc) and diffuse cutaneous (dcSSc) forms …

Serum markers in systemic sclerosis with cardiac involvement

N Gokcen - Clinical Rheumatology, 2023 - Springer
Cardiac involvement in systemic sclerosis is a common clinical entity that may range from
subclinical to life-threatening complications. The classification of cardiac involvement may …

Association between systemic sclerosis and left ventricle dysfunction: Findings from observational studies

W Yan, Q Luo, Q Nie, H Wang, J Wu - Heliyon, 2023 - cell.com
Objectives Cardiac involvement is common in systemic sclerosis (SSc) patients. In this study,
we aimed to systematically evaluate the relationship between SSc and left ventricular …

Multidisciplinary team discussion: the emerging gold standard for management of cardiopulmonary complications of connective tissue disease

JL Fairley, L Ross, A Burns, D Prior… - Internal Medicine …, 2023 - Wiley Online Library
Cardiopulmonary complications of connective tissue diseases (CTDs), particularly
pulmonary arterial hypertension (PAH) and interstitial lung disease (ILD), are major …

Late-age onset systemic sclerosis—clinical and serological characteristics

E Wielosz, K Wiąk-Walerowicz, E Łyś, A Lipska… - Clinical …, 2024 - Springer
The clinical course and serological profile of the late-age onset systemic sclerosis (LAO
SSc) and the early-age onset SSc (EAO SSc) was compared. The study enrolled 157 …

[HTML][HTML] Systemic sclerosis-associated interstitial lung disease: Diagnostic approaches and challenges

JL Fairley, NSL Goh, M Nikpour - Revista Colombiana de Reumatología …, 2024 - Elsevier
Interstitial lung disease (ILD) is a leading cause of both morbidity and mortality in systemic
sclerosis (SSc). Radiographic lung abnormalities on high-resolution computed tomography …