All the “RAGE” in lung disease: The receptor for advanced glycation endproducts (RAGE) is a major mediator of pulmonary inflammatory responses

EA Oczypok, TN Perkins, TD Oury - Paediatric respiratory reviews, 2017 - Elsevier
The receptor for advanced glycation endproducts (RAGE) is a pro-inflammatory pattern
recognition receptor (PRR) that has been implicated in the pathogenesis of numerous …

European protocols for the diagnosis and initial treatment of interstitial lung disease in children

A Bush, S Cunningham, J De Blic, A Barbato… - Thorax, 2015 - thorax.bmj.com
Interstitial lung disease in children (chILD) is rare, and most centres will only see a few
cases/year. There are numerous possible underlying diagnoses, with specific and non …

Systemic juvenile idiopathic arthritis–associated lung disease: characterization and risk factors

GS Schulert, S Yasin, B Carey, C Chalk… - Arthritis & …, 2019 - Wiley Online Library
Objective Systemic juvenile idiopathic arthritis (JIA) is associated with a recently recognized,
albeit poorly defined and characterized, lung disease (LD). The objective of this study was to …

Evaluation and management of pulmonary hypertension in children with bronchopulmonary dysplasia

U Krishnan, JA Feinstein, I Adatia, ED Austin… - The Journal of …, 2017 - jpeds.com
Methods A working group from PPHNet specialists that included neonatologists,
cardiologists, pulmonologists, and intensivists was established to create this document …

European Respiratory Society statement on familial pulmonary fibrosis

R Borie, C Kannengiesser, K Antoniou… - European …, 2023 - Eur Respiratory Soc
Genetic predisposition to pulmonary fibrosis has been confirmed by the discovery of several
gene mutations that cause pulmonary fibrosis. Although genetic sequencing of familial …

LungMAP: the molecular atlas of lung development program

ME Ardini-Poleske, RF Clark… - … of Physiology-Lung …, 2017 - journals.physiology.org
The National Heart, Lung, and Blood Institute is funding an effort to create a molecular atlas
of the developing lung (LungMAP) to serve as a research resource and public education …

[HTML][HTML] Etiologic classification of diffuse parenchymal (interstitial) lung diseases

M Griese - Journal of Clinical Medicine, 2022 - mdpi.com
Interstitial lung diseases (ILD) or diffuse parenchymal lung diseases (DPLD) comprise a
large number of disorders. Disease definition and classification allow advanced and …

[HTML][HTML] Club cell secreted protein CC16: potential applications in prognosis and therapy for pulmonary diseases

S Almuntashiri, Y Zhu, Y Han, X Wang… - Journal of clinical …, 2020 - mdpi.com
Club cell secretory protein (CC16) is encoded by the SCGB1A1 gene. It is also known as
CC10, secretoglobin, or uteroglobin. CC16 is a 16 kDa homodimeric protein secreted …

Diseases of pulmonary surfactant homeostasis

JA Whitsett, SE Wert, TE Weaver - Annual Review of Pathology …, 2015 - annualreviews.org
Advances in physiology and biochemistry have provided fundamental insights into the role
of pulmonary surfactant in the pathogenesis and treatment of preterm infants with respiratory …

[HTML][HTML] Diagnostic workup of childhood interstitial lung disease

N Nathan, M Griese, K Michel, J Carlens… - European …, 2023 - Eur Respiratory Soc
Childhood interstitial lung diseases (chILDs) are rare and heterogeneous diseases with
significant morbidity and mortality. An accurate and quick aetiological diagnosis may …