Impaired tissue homing by the Ikzf3N159S variant is mediated by interfering with Ikaros function

J Chang, M Yamashita, AK Padhi, KYJ Zhang… - Frontiers in …, 2023 - frontiersin.org
AIOLOS, encoded by IKZF3, is a member of the IKZF family of proteins that plays an
important role in regulating late B-cell differentiation. Human individuals heterozygous for …

AIOLOS-Associated Inborn Errors of Immunity

M Yamashita, T Morio - Journal of Clinical Immunology, 2024 - Springer
AIOLOS, encoded by the IKZF3 gene, belongs to the Ikaros zinc finger transcription factor
family and plays a pivotal role in regulating lymphocyte development. Recently …

Helios—Illuminating the way for lymphocyte self‐control

I Hetemäki, TP Arstila, E Kekäläinen - Immunology, 2024 - Wiley Online Library
Transcription factor Helios, encoded by the IKZF2 gene, has an important role in regulatory T
cells by stabilizing their suppressive phenotype. While Helios is prominently expressed in …

Exome variant prioritization in a large cohort of hearing-impaired individuals indicates IKZF2 to be associated with non-syndromic hearing loss and guides future …

HM Velde, M Vaseghi-Shanjani, JJ Smits… - Human Genetics, 2024 - Springer
Although more than 140 genes have been associated with non-syndromic hereditary
hearing loss (HL), at least half of the cases remain unexplained in medical genetic testing …

A germline heterozygous dominant negative IKZF2 variant causing syndromic primary immune regulatory disorder and ICHAD

HY Lu, M Vaseghi-Shanjani, AJ Lam, M Sharma… - medRxiv, 2023 - medrxiv.org
Monogenic defects that impair the control of inflammation and tolerance lead to profound
immune dysregulation, including autoimmunity and atopy. Studying these disorders reveals …