[HTML][HTML] Pathogenesis of IgA vasculitis: an up-to-date review

Y Song, X Huang, G Yu, J Qiao, J Cheng, J Wu… - Frontiers in …, 2021 - frontiersin.org
Immunoglobin A (IgA) vasculitis (IgAV), formerly called the Henoch-Schönlein purpura
(HSP), is a small vessel vasculitis, characterized by IgA1-dominant immune deposition at …

Henoch-Schönlein purpura in children: an updated review

AKC Leung, B Barankin, KF Leong - Current pediatric reviews, 2020 - ingentaconnect.com
Background: Henoch-Schönlein purpura (HSP) is an IgA-mediated systemic smallvessel
vasculitis with a predilection for the skin, gastrointestinal tract, joints, and kidneys. It is the …

The expanded spectrum of arthritis in children with familial Mediterranean fever

PO Avar-Aydın, ZB Ozcakar, F Aydın, HD Karakas… - Clinical …, 2022 - Springer
Abstract Introduction Familial Mediterranean fever (FMF) is the most common monogenic
autoinflammatory disease that can present with various forms of arthritis. This retrospective …

Inflammatory comorbidities ın the largest pediatric Familial Mediterranean fever cohort: a multicenter retrospective study of Pediatric Rheumatology Academy (PeRA) …

S Ozdel, T Coşkuner, F Demirkan, R Torun… - Clinical …, 2024 - Springer
Aim The aim of this study was to investigate the frequency and type of FMF-associated
inflammatory diseases in a large FMF pediatric patients and to compare them to those FMF …

Associations of MEFV gene variants, IL-33, and sST2 with the risk of Henoch-Schönlein purpura in children

Y Ruan, L Xie - Heliyon, 2024 - cell.com
Abstract Objective Henoch-Schönlein purpura (HSP) is the most common systemic vasculitis
in children. HSP is a multifactorial inflammatory disease, but its pathogenesis is still unclear …

Effect of MEFV variants on the presentation and clinical course of Henoch-Schonlein purpura in children?

C Açarı, M Bayram, G Yıldız, S Kavukçu… - Dokuz Eylül Üniversitesi …, 2023 - dergipark.org.tr
Objective: We aimed to evaluate MEFV mutation frequency and the effects of MEFV
mutations on the clinical course including renal involvement in children with Henoch …

Immunoglobulin A vasculitis in a Japanese patient with complete familial Mediterranean fever carrying MEFV exon 10 mutation

T Sasajima, Y Fujita, Y Ejiri, T Suzuki… - The Tohoku Journal of …, 2021 - jstage.jst.go.jp
Immunoglobulin A (IgA) vasculitis is a systemic small-vessel vasculitis involving the skin,
kidney, joints, and gastrointestinal tract. Familial Mediterranean fever (FMF) is the most …

Intravenous immunoglobulin therapy in immunoglobulin A vasculitis with gastrointestinal tract involvement

N Öner, E Çelikel, ZE Tekin, V Güngörer, T Kurt… - Clinical and …, 2023 - Springer
Objective The aim of this study is to evaluate the outcomes of patients who received
intravenous immunoglobulin (IVIG) for immunoglobulin A vasculitis (IgAV) with …

Clinical Associations of E148Q Heterozygosity: What to Expect From E148Q?

B Küçükali, EÖ Bayraktar, Ç Yıldız… - JCR: Journal of …, 2024 - journals.lww.com
Objective The exact effects of MEFV variants on inflammation are still under investigation,
and reports on variants of unknown significance, particularly the E148Q variant, have been …

[PDF][PDF] Initial manifestations and short term follow-up results of Henoch-Schönlein purpura in children: A report from two centers.

K Ozturk, M Cakan - Northern Clinics of İstanbul, 2020 - jag.journalagent.com
ABSTRACT OBJECTIVE: This retrospective observational study aims to demonstrate initial
signs and symptoms of Henoch-Schönlein purpura (HSP), search for risk factors for …