Personalized management of pheochromocytoma and paraganglioma

S Nölting, N Bechmann, D Taieb… - Endocrine …, 2022 - academic.oup.com
Pheochromocytomas/paragangliomas are characterized by a unique molecular landscape
that allows their assignment to clusters based on underlying genetic alterations. With around …

Current management of pheochromocytoma/paraganglioma: a guide for the practicing clinician in the era of precision medicine

S Nölting, M Ullrich, J Pietzsch, CG Ziegler… - Cancers, 2019 - mdpi.com
Pheochromocytomas and paragangliomas (PCC/PGLs) are rare, mostly catecholamine-
producing neuroendocrine tumors of the adrenal gland (PCCs) or the extra-adrenal …

Multidisciplinary practice guidelines for the diagnosis, genetic counseling and treatment of pheochromocytomas and paragangliomas

R García-Carbonero, F Matute Teresa… - Clinical and …, 2021 - Springer
Pheochromocytomas and paragangliomas (PPGLs) are rare neuroendocrine tumors that
arise from chromaffin cells of the adrenal medulla and the sympathetic/parasympathetic …

The North American Neuroendocrine Tumor Society consensus guidelines for surveillance and management of metastatic and/or unresectable pheochromocytoma …

L Fishbein, J Del Rivero, T Else, JR Howe, SL Asa… - Pancreas, 2021 - journals.lww.com
This manuscript is the result of the North American Neuroendocrine Tumor Society
consensus conference on the medical management and surveillance of metastatic and …

Targeted therapies in pheochromocytoma and paraganglioma

K Wang, J Crona, F Beuschlein… - The Journal of …, 2022 - academic.oup.com
Molecular targeted therapy plays an increasingly important role in the treatment of metastatic
pheochromocytomas and paragangliomas (PPGLs), which are rare tumors but remain …

Metastatic pheochromocytomas and abdominal paragangliomas

D Granberg, CC Juhlin… - The journal of clinical …, 2021 - academic.oup.com
Abstract Context Pheochromocytomas and paragangliomas (PPGLs) are believed to harbor
malignant potential; about 10% to 15% of pheochromocytomas and up to 50% of abdominal …

Pheochromocytoma: a changing perspective and current concepts

A Kiriakopoulos, P Giannakis… - … in endocrinology and …, 2023 - journals.sagepub.com
This article aims to review current concepts in diagnosing and managing
pheochromocytoma and paraganglioma (PPGL). Personalized genetic testing is vital, as 40 …

Pheochromocytomas and abdominal paragangliomas: a practical guidance

J Calissendorff, CC Juhlin, I Bancos, H Falhammar - Cancers, 2022 - mdpi.com
Simple Summary Pheochromocytomas and abdominal paragangliomas (PPGLs) are rare.
They can be discovered incidentally by imaging with computed tomography or magnetic …

Management of phaeochromocytoma and paraganglioma in patients with germline SDHB pathogenic variants: an international expert Consensus statement

D Taïeb, S Nölting, ND Perrier, M Fassnacht… - Nature Reviews …, 2024 - nature.com
Adult and paediatric patients with pathogenic variants in the gene encoding succinate
dehydrogenase (SDH) subunit B (SDHB) often have locally aggressive, recurrent or …

[HTML][HTML] Pheochromocytoma/paraganglioma: recent updates in genetics, biochemistry, immunohistochemistry, metabolomics, imaging and therapeutic options

K Antonio, MMN Valdez, L Mercado-Asis, D Taïeb… - Gland …, 2020 - ncbi.nlm.nih.gov
Pheochromocytomas and paragangliomas (PPGLs), rare chromaffin/neural crest cell tumors,
are commonly benign in their clinical presentation. However, there are a number of cases …