Congenital fibrinogen disorders (CFDs) are a heterogeneous group of rare congenital
quantitative and/or qualitative fibrinogen deficiencies. The spectrum of molecular anomalies …

A bleeding tendency is one of the most common complaints observed by hematologists. It is
challenging to differentiate a clinically insignificant bleeding from a bleeding phenotype that …

Background Factor (F) XI deficiency is a rare bleeding disorder with a poor correlation
between bleeding tendency and FXI level. Management of pregnant women with FXI …

Background Despite the wide use of bleeding scores and the reliability of clotting factor level
measurement, bleeding risk stratification before surgery remains challenging in patients with …

Inherited factor coagulation deficiencies and vascular bleeding disorders, associated with
bleeding of various severity, are often classified as rare bleeding disorders (RBDs). These …

Interventions: To prevent bleeding, a total of 8 doses of recombinant activated factor VII and
1 dose of fresh frozen plasma were administered as the perioperative replacement therapy …

Introduction Due to their low prevalence, rare bleeding disorders (RBDs) remain poorly
characterized. Aim To gain insight of RBDs through our clinical practice. Methods …

Moderate factor XI deficiency and neuraxial procedures in an obstetric cohort: a retrospective
study (2014–2021) - ScienceDirect Skip to main contentSkip to article Elsevier logo Journals & …

Quantitative fibrinogen disorders, including afibrinogenemia and hypofibrinogenemia, are
defined by the complete absence or reduction of fibrinogen, respectively. The diagnosis is …

Abstract Background Factor (F) XI deficiency is a rare bleeding disorder with a poor
correlation between bleeding tendency and FXI level. Management of pregnant women with …